[Kennedy disease: report of 2 cases]. / Doença de Kennedy: relato de dois casos.
Arq Neuropsiquiatr
; 53(3-A): 471-4, 1995 Sep.
Article
em Pt
| MEDLINE
| ID: mdl-8540824
We report two cases of Kennedy's disease (muscle weakness, amyotrophy, intentional tremor, endocrine abnormalities, and denervation signs at electromyography). This entity must be differentiated from other motor neuron disorders by the genetic pattern (X-liked recessive), gynecomastia, testicular atrophy, oligospermia and good prognosis. A discussion about the clinical pattern and evolution is made.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Atrofia Muscular Espinal
Tipo de estudo:
Diagnostic_studies
/
Prognostic_studies
Limite:
Adolescent
/
Adult
/
Humans
/
Male
Idioma:
Pt
Revista:
Arq Neuropsiquiatr
Ano de publicação:
1995
Tipo de documento:
Article
País de publicação:
Alemanha