[Peutz-Jeghers syndrome and adenocarcinoma. Report of a case]. / Síndrome de Peutz-Jeghers e adenocarcinoma. Relato de caso.
Arq Gastroenterol
; 31(4): 145-8, 1994.
Article
em Pt
| MEDLINE
| ID: mdl-7575174
Peutz-Jeghers syndrome is a rare disease, characterized by autosomic inheritance, presenting skin stain and hamartomatous polyps. We report one case of Peutz-Jeghers syndrome and duodenal adenocarcinoma in a young male who presented with liver metastasis and pancreatic invasion. Such association is reported to be presented in 5% of patients with the syndrome. The reasons of such association are unknown, being possible that: 1) there is malignant degeneration of a adenomatous polyp; 2) malignant degeneration of a hamartomatous polyp, or 3) adenomatous portion of a hamartomatous polyp could undergo malignant transformation.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Síndrome de Peutz-Jeghers
/
Adenocarcinoma
/
Neoplasias Duodenais
Limite:
Adult
/
Humans
/
Male
Idioma:
Pt
Revista:
Arq Gastroenterol
Ano de publicação:
1994
Tipo de documento:
Article
País de publicação:
Brasil