Prenatal treatment of congenital adrenal hyperplasia resulting from 21-hydroxylase deficiency.
J Pediatr
; 105(5): 799-803, 1984 Nov.
Article
em En
| MEDLINE
| ID: mdl-6334149
In an attempt to prevent in utero virilization of female fetuses with 21-hydroxylase deficiency, six mothers at risk were treated with either hydrocortisone (n = 1) or dexamethasone (n = 5) in early pregnancy. Treatment was continued to term in the two pregnancies in which the diagnosis of an affected female fetus was confirmed. In patient 1 (hydrocortisone treatment) fetal adrenal suppression was only partial but the external genitalia were only slightly abnormal. In patient 2 (dexamethasone treatment) fetal adrenal suppression was achieved and the external genitalia were normal at birth. These encouraging results open a new prospect for treating congenital adrenal hyperplasia in utero.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Cuidado Pré-Natal
/
Esteroide Hidroxilases
/
Hiperplasia Suprarrenal Congênita
Limite:
Adult
/
Female
/
Humans
/
Newborn
/
Pregnancy
Idioma:
En
Revista:
J Pediatr
Ano de publicação:
1984
Tipo de documento:
Article
País de publicação:
Estados Unidos