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Idiopathic infantile arterial calcification in siblings: radiologic diagnosis and successful treatment.
J Pediatr ; 92(3): 401-5, 1978 Mar.
Article em En | MEDLINE | ID: mdl-416189
Idiopathic infantile arterial calcification is a disorder of unknown etiology manifested by widespread arterial calcification. This usually leads to early death from coronary artery occlusion. In 12 of the 75 cases in the literature, radiographs were taken and it was possible to make the diagnosis in them all. We present two patients, siblings, in whom the diagnosis was established radiologically. The nature of the calcium deposits was studied in one of the infants and proved to be calcium hydroxyapatite. Therapy with diphosphonate was apparently successful in the other child.
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Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Arteriosclerose / Calcinose / Doenças do Recém-Nascido Tipo de estudo: Diagnostic_studies Limite: Female / Humans / Male / Newborn / Pregnancy Idioma: En Revista: J Pediatr Ano de publicação: 1978 Tipo de documento: Article País de publicação: Estados Unidos
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Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Arteriosclerose / Calcinose / Doenças do Recém-Nascido Tipo de estudo: Diagnostic_studies Limite: Female / Humans / Male / Newborn / Pregnancy Idioma: En Revista: J Pediatr Ano de publicação: 1978 Tipo de documento: Article País de publicação: Estados Unidos