Adult ocular adnexal xanthogranulomatous disease associated with immunoglobulin G4-related disease: an unusual association.
Reumatismo
; 76(1)2024 Mar 22.
Article
em En
| MEDLINE
| ID: mdl-38523581
ABSTRACT
Adult-onset xanthogranuloma (AOX) and immunoglobulin G4-related disease (IgG4-RD) are uncommon fibrosing conditions that may exhibit localized ocular manifestations and occasionally systemic symptoms. These conditions exhibit overlapping clinical and histological features, suggesting a potential correlation between them, although their exact relationship remains unclear. This paper presents the case of a black male patient exhibiting typical histological indications of both AOX and IgG4-RD. The patient responded positively to corticosteroid treatment.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Neoplasias Hematológicas
/
Doença Relacionada a Imunoglobulina G4
Limite:
Adult
/
Humans
/
Male
Idioma:
En
Revista:
Reumatismo
Ano de publicação:
2024
Tipo de documento:
Article
País de afiliação:
El Salvador
País de publicação:
Itália