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Bladder and urethral duplication and a bladder exstrophy plate with omphalocele in a female child.
Freitas Filho, Luiz G; Carvalho Fonseca, Ana Carolina; Guerreiro Paiva, Taynara Roberta; Stephane de Medeiros Jerônimo, Bárbara; Magalhães, Raphael Miranda; Gomes Abreu, Maria Cristina; Budib, Luiz J.
Afiliação
  • Freitas Filho LG; Professor of Urology Universidade Federal de São Paulo, Visiting Professor, Hospital Santa Marcelina, Brazil.
  • Carvalho Fonseca AC; Resident in Pediatric Surgery, Hospital Santa Marcelina, Brazil.
  • Guerreiro Paiva TR; Resident in Pediatric Surgery, Hospital Santa Marcelina, Brazil.
  • Stephane de Medeiros Jerônimo B; Resident in Pediatric Surgery, Hospital Santa Marcelina, Brazil.
  • Magalhães RM; Resident in Pediatric Surgery, Hospital Santa Marcelina, Brazil.
  • Gomes Abreu MC; Department of Pediatric Surgery, Hospital Santa Marcelina, Brazil.
  • Budib LJ; Department of Urology, Hospital Santa Marcelina, Brazil.
Urol Case Rep ; 39: 101769, 2021 Nov.
Article em En | MEDLINE | ID: mdl-34285880
The Exstrophy - Epispadias Complex (EEC) is a spectrum of rare congenital malformations involving the urinary, genital and musculoskeletal systems. We present an atypical or variant case of EEC in which a bladder plate is found involving a small omphalocele, separated pubic bones and bladder and urethral duplication. The treatment had a favorable outcome, with bladder control and the child voiding normally. Perhaps the best accepted embryonic theory to explain exstrophy and its variants should be reviewed as it fails to satisfactorily explain the alterations we found.
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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Idioma: En Revista: Urol Case Rep Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Brasil País de publicação: Estados Unidos

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Idioma: En Revista: Urol Case Rep Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Brasil País de publicação: Estados Unidos