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Multidisciplinary practice guidelines for the diagnosis, genetic counseling and treatment of pheochromocytomas and paragangliomas.
Garcia-Carbonero, R; Matute Teresa, F; Mercader-Cidoncha, E; Mitjavila-Casanovas, M; Robledo, M; Tena, I; Alvarez-Escola, C; Arístegui, M; Bella-Cueto, M R; Ferrer-Albiach, C; Hanzu, F A.
Afiliação
  • Garcia-Carbonero R; Medical Oncology Department, Hospital Universitario 12 de Octubre, Instituto de Investigación Sanitaria Hospital 12 de Octubre (imas12), UCM, CNIO, CIBERONC, Avda Cordoba km 5.4, 28041, Madrid, Spain. rgcarbonero@gmail.com.
  • Matute Teresa F; Radiology Department, Hospital Clínico San Carlos, Madrid, Spain.
  • Mercader-Cidoncha E; Endocrine and Metabolic Surgery Unit, General and Digestive Surgery Department, Hospital General Universitario Gregorio Marañón, Madrid, Spain.
  • Mitjavila-Casanovas M; Nuclear Medicine Department, Hospital Universitario Puerta de Hierro, Majadahonda, Spain.
  • Robledo M; Grupo de Trabajo de Endocrino de la SEMNIM, Madrid, Spain.
  • Tena I; Hereditary Endocrine Cancer Group, Spanish National Cancer Research Center, Madrid, Spain.
  • Alvarez-Escola C; Centro de Investigación Biomédica en Red de Enfermedades Raras (CIBERER), Madrid, Spain.
  • Arístegui M; Scientific Department, Medica Scientia Innovation Research (MedSIR CORP), Ridgewood, NJ, USA.
  • Bella-Cueto MR; Medical Oncology Department, Hospital Provincial, Castellon, Spain.
  • Ferrer-Albiach C; Neuroendocrinology Unit, Endocrinology and Nutrition Department, Hospital Universitario la Paz, Madrid, Spain.
  • Hanzu FA; ENT Department, Hospital General Universitario Gregorio Marañón, Madrid, Spain.
Clin Transl Oncol ; 23(10): 1995-2019, 2021 Oct.
Article em En | MEDLINE | ID: mdl-33959901
Pheochromocytomas and paragangliomas (PPGLs) are rare neuroendocrine tumors that arise from chromaffin cells of the adrenal medulla and the sympathetic/parasympathetic neural ganglia, respectively. The heterogeneity in its etiology makes PPGL diagnosis and treatment very complex. The aim of this article was to provide practical clinical guidelines for the diagnosis and treatment of PPGLs from a multidisciplinary perspective, with the involvement of the Spanish Societies of Endocrinology and Nutrition (SEEN), Medical Oncology (SEOM), Medical Radiology (SERAM), Nuclear Medicine and Molecular Imaging (SEMNIM), Otorhinolaryngology (SEORL), Pathology (SEAP), Radiation Oncology (SEOR), Surgery (AEC) and the Spanish National Cancer Research Center (CNIO). We will review the following topics: epidemiology; anatomy, pathology and molecular pathways; clinical presentation; hereditary predisposition syndromes and genetic counseling and testing; diagnostic procedures, including biochemical testing and imaging studies; treatment including catecholamine blockade, surgery, radiotherapy and radiometabolic therapy, systemic therapy, local ablative therapy and supportive care. Finally, we will provide follow-up recommendations.
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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Paraganglioma / Feocromocitoma / Neoplasias das Glândulas Suprarrenais Tipo de estudo: Diagnostic_studies / Guideline / Prognostic_studies Limite: Humans País/Região como assunto: Europa Idioma: En Revista: Clin Transl Oncol Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Espanha País de publicação: Itália
Texto completo
Adicionar na Minha BVS
Imprimir
XML
PubMed Links
Buscar no Google

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Paraganglioma / Feocromocitoma / Neoplasias das Glândulas Suprarrenais Tipo de estudo: Diagnostic_studies / Guideline / Prognostic_studies Limite: Humans País/Região como assunto: Europa Idioma: En Revista: Clin Transl Oncol Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Espanha País de publicação: Itália