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Retinal lipemia as expression of hyperchylomicronemia syndrome.
Ortiz de Salido-Menchaca, Jon; Tazón-Varela, Manuel Antonio; de la Hera-Vegas, David; Herreras-Martínez, Rosa; Álvarez-Agudelo, Sergio Andrés; Arencibia-Hernández, Nuria.
Afiliação
  • Ortiz de Salido-Menchaca J; Hospital de Laredo, Servicio de Urgencias. Cantabria, España. Hospital de Laredo Servicio de Urgencias Cantabria España.
  • Tazón-Varela MA; Hospital de Laredo, Servicio de Urgencias. Cantabria, España. Hospital de Laredo Servicio de Urgencias Cantabria España.
  • de la Hera-Vegas D; Instituto de Investigación Sanitaria Valdecilla (IDIVAL), Área Transversal- Grupo Salud Comunitaria. Cantabria, España Instituto de Investigación Sanitaria Valdecilla (IDIVAL) Área Transversal- Grupo Salud Comunitaria Cantabria España.
  • Herreras-Martínez R; Hospital de Laredo, Servicio de Oftalmología, Cantabria, España. Hospital de Laredo Servicio de Oftalmología Cantabria España.
  • Álvarez-Agudelo SA; Hospital Universitario Marqués de Valdecilla, Servicio de Medicina Interna, Cantabria, España. Hospital Universitario Marqués de Valdecilla Servicio de Medicina Interna Cantabria España.
  • Arencibia-Hernández N; Hospital de Laredo, Servicio de Urgencias. Cantabria, España. Hospital de Laredo Servicio de Urgencias Cantabria España.
Colomb Med (Cali) ; 52(1): e7024059, 2021 Mar 30.
Article em En | MEDLINE | ID: mdl-33911323
CASE DESCRIPTION: Case of lipemia retinalis secondary to hyperchylomicronemia in a 40-year-old man with a history of total body irradiation and immunosuppressive treatment that was attended in this hospital due to decreased visual acuity and abdominal pain. CLINICAL FINDINGS: Hyperchylomicronemia caused the development of acute pancreatitis and lipemia retinalis. The latter is an infrequent ocular manifestation that reflects excessive triglyceride blood levels in the organism (>2,000 mg/dL). Lipemia retinalis is characterized by the accumulation of chylomicrons in the retinal vessels, which gives them a white and creamy appearance in direct retinal ophthalmoscopy. The initial clinical suspicion of hyperchylomicronemia was based on the visualization of the supernatant in the analytical tube. TREATMENT AND RESULT: In the absence of definitive biochemical results, and owing to the need for special processing of the sample, lipid-lowering treatment and serum therapy were established after ophthalmological confirmation of lipemia retinalis, with subsequent full recovery of visual acuity. CLINICAL RELEVANCE: Given the initial difficulty to determine the accurate triglyceride levels in this kind of patient, early visualization of milky-colored retinal vessels on a salmon-colored eye fundus can help develop an early clinical suspicion of severe hyperchylomicronemia and contribute to limit the severity of complications.
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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Pancreatite / Doenças Retinianas / Hipertrigliceridemia / Hiperlipidemias Tipo de estudo: Diagnostic_studies / Etiology_studies Limite: Adult / Humans / Male Idioma: En Revista: Colomb Med (Cali) Ano de publicação: 2021 Tipo de documento: Article País de publicação: Colômbia

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Pancreatite / Doenças Retinianas / Hipertrigliceridemia / Hiperlipidemias Tipo de estudo: Diagnostic_studies / Etiology_studies Limite: Adult / Humans / Male Idioma: En Revista: Colomb Med (Cali) Ano de publicação: 2021 Tipo de documento: Article País de publicação: Colômbia