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Cleidocranial dysplasia, a rare skeletal disorder with failure of the cranial closure: case-based update.
Azevedo Almeida, Laryssa C; Faraj de Lima, Franklin B; Matushita, Hamilton; Valença, Marcelo M; Ferreira Castro, Tamireis L; de Mendonça, Rafael N.
Afiliação
  • Azevedo Almeida LC; Centre for Neurology and Neurosurgery at Santa Casa de Misericórdia de Belo Horizonte, Belo Horizonte, Minas Gerais, Brazil. laryssazevedo@hotmail.com.
  • Faraj de Lima FB; Centre for Neurology and Neurosurgery at Santa Casa de Misericórdia de Belo Horizonte, Belo Horizonte, Minas Gerais, Brazil.
  • Matushita H; Division of Neurological Surgery, University of São Paulo, Sao Paulo, Brazil.
  • Valença MM; Neurology and Neurosurgery Unit, Department of Neuropsychiatry, Federal University of Pernambuco, Recife, Pernambuco, Brazil.
  • Ferreira Castro TL; University Center of Belo Horizonte, Belo Horizonte, Minas Gerais, Brazil.
  • de Mendonça RN; University Center of Belo Horizonte, Belo Horizonte, Minas Gerais, Brazil.
Childs Nerv Syst ; 36(12): 2913-2918, 2020 12.
Article em En | MEDLINE | ID: mdl-32734401
BACKGROUND AND AIM: Cleidocranial dysplasia is a rare disorder of skeletal development that mainly promotes, among other malformations, inadequate development of clavicles and failure in cranial closure. In this affection, the role of neurosurgery in addressing cranial defects is rarely discussed. MATERIAL AND METHODS: We conducted an extensive review of the literature using the PubMed database, giving a greater focus to publications in the field of neurosurgery. Additionally, we report a case of a 2-year-old female child with cleidocranial dysplasia. RESULTS: In our review, we encountered several cases of orthodontic implications but a few cases on cranial defect approach. CONCLUSION: The articles present literature that is unanimous on the recommendation of expectant conduct in children since the cranial block can occur spontaneously, even if the delayed form. In our approach, we opted for an expected strategy concerning the cranial defect, using a helmet made for brain protection. We also made the referral for multidisciplinary monitoring of pediatrics, neuropediatrics, ophthalmology, dentistry, and orthopedics.
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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Displasia Cleidocraniana Limite: Child, preschool / Female / Humans Idioma: En Revista: Childs Nerv Syst Assunto da revista: NEUROLOGIA / PEDIATRIA Ano de publicação: 2020 Tipo de documento: Article País de afiliação: Brasil País de publicação: Alemanha
Texto completo
Adicionar na Minha BVS
Imprimir
XML
PubMed Links
Buscar no Google

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Displasia Cleidocraniana Limite: Child, preschool / Female / Humans Idioma: En Revista: Childs Nerv Syst Assunto da revista: NEUROLOGIA / PEDIATRIA Ano de publicação: 2020 Tipo de documento: Article País de afiliação: Brasil País de publicação: Alemanha