Complete form of pachydermoperiostosis.
An Bras Dermatol
; 95(1): 98-101, 2020.
Article
em En
| MEDLINE
| ID: mdl-31889594
Pachydermoperiostosis (PDP) or primary hypertrophic osteoarthropathy (PHO) is a rare hereditary disease characterized by digital clubbing, pachydermia, and periostosis. Its pathogenesis is uncertain and the diagnosis is based on clinical and radiological data. A complete form of the syndrome is reported in a male patient with disease onset in adolescence, with compatible clinical and radiological findings, presenting the three cardinal findings as well as other associated manifestations, such as hyperhidrosis and acne.
Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Osteoartropatia Hipertrófica Primária
Limite:
Adult
/
Humans
/
Male
Idioma:
En
Revista:
An Bras Dermatol
Ano de publicação:
2020
Tipo de documento:
Article
País de publicação:
Espanha