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[Neurofibromatosis and extensive intracranial arterial occlusive disease (moyamoya disease). Report of a case]. / Neurofibromatose e doença arterial oclusiva intracraniana extensa (doença de moya-moya). Registro de um caso.
Arq Neuropsiquiatr ; 44(4): 395-400, 1986 Dec.
Article em Pt | MEDLINE | ID: mdl-3111450
A 33-year-old female with neurofibromatosis and intracranial vascular lesions of the Moya-Moya type is reported. Clinical and angiographic aspects of both syndromes are discussed with respect to earlier reports of this rare association, with the conclusion that it produces slow intellectual and motor deterioration in adolescents or young adults. There are no specific guidelines to therapy, and the prognosis is mixed, some patients ceasing to progress at least for a few years.
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Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Arteriopatias Oclusivas / Neurofibromatose 1 / Doença de Moyamoya Tipo de estudo: Guideline / Prognostic_studies Limite: Adult / Female / Humans Idioma: Pt Revista: Arq Neuropsiquiatr Ano de publicação: 1986 Tipo de documento: Article País de publicação: Alemanha
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Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Arteriopatias Oclusivas / Neurofibromatose 1 / Doença de Moyamoya Tipo de estudo: Guideline / Prognostic_studies Limite: Adult / Female / Humans Idioma: Pt Revista: Arq Neuropsiquiatr Ano de publicação: 1986 Tipo de documento: Article País de publicação: Alemanha