[Neurofibromatosis and extensive intracranial arterial occlusive disease (moyamoya disease). Report of a case]. / Neurofibromatose e doença arterial oclusiva intracraniana extensa (doença de moya-moya). Registro de um caso.
Arq Neuropsiquiatr
; 44(4): 395-400, 1986 Dec.
Article
em Pt
| MEDLINE
| ID: mdl-3111450
A 33-year-old female with neurofibromatosis and intracranial vascular lesions of the Moya-Moya type is reported. Clinical and angiographic aspects of both syndromes are discussed with respect to earlier reports of this rare association, with the conclusion that it produces slow intellectual and motor deterioration in adolescents or young adults. There are no specific guidelines to therapy, and the prognosis is mixed, some patients ceasing to progress at least for a few years.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Arteriopatias Oclusivas
/
Neurofibromatose 1
/
Doença de Moyamoya
Tipo de estudo:
Guideline
/
Prognostic_studies
Limite:
Adult
/
Female
/
Humans
Idioma:
Pt
Revista:
Arq Neuropsiquiatr
Ano de publicação:
1986
Tipo de documento:
Article
País de publicação:
Alemanha