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An unusual variant of atrophic dermatofibrosarcoma protuberans.
Aragão, Simone Silva da Costa; Leite, Everson José Dos Santos; Cardoso, Alberto Eduardo Cox; Houly, Ricardo Luiz Simões.
Afiliação
  • Aragão SSDC; Hospital Universitário Prof. Alberto Antunes, Universidade Federal de Alagoas, Maceió, AL, Brazil.
  • Leite EJDS; Hospital Universitário Prof. Alberto Antunes, Universidade Federal de Alagoas, Maceió, AL, Brazil.
  • Cardoso AEC; Hospital Universitário Prof. Alberto Antunes, Universidade Federal de Alagoas, Maceió, AL, Brazil.
  • Houly RLS; Hospital Universitário Prof. Alberto Antunes, Universidade Federal de Alagoas, Maceió, AL, Brazil.
An Bras Dermatol ; 93(2): 282-284, 2018 03.
Article em En | MEDLINE | ID: mdl-29723383
Dermatofibrosarcoma protuberans is an uncommon neoplasm that is most often seen in young adults. The most common clinical presentation is the protruding form; however, other subtypes are known, such as the atrophic. In 2012 there were only 33 reports of this variant in the literature. Many cases of Dermatofibrosarcoma protuberans in children are only discovered in adulthood because they were not diagnosed early. Due the high morbidity, we raise the need for attention from the dermatologist to recognize uncommon neoplasms in the clinical practice. We report a case of a 15-year-old patient diagnosed with atrophic Dermatofibrosarcoma protuberans on the back.
Assuntos

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Neoplasias Cutâneas / Dermatofibrossarcoma Limite: Adolescent / Humans / Male Idioma: En Revista: An Bras Dermatol Ano de publicação: 2018 Tipo de documento: Article País de afiliação: Brasil País de publicação: Espanha

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Neoplasias Cutâneas / Dermatofibrossarcoma Limite: Adolescent / Humans / Male Idioma: En Revista: An Bras Dermatol Ano de publicação: 2018 Tipo de documento: Article País de afiliação: Brasil País de publicação: Espanha