8-OHdG, 8-hydroxy-2'-deoxyguanosine; Cr, creatinine; DI, damage index; DTNB, 5,5'-dithiobis(2-nitrobenzoic acid); ELISA, enzyme-linked immunoassay; ERT, enzyme replacement therapy; Endo III, endonuclease III; FU, fluorescence units; GAGs, glycosaminoglycans; GALNS, N-acetylgalactosamine-6-sulfatase; GCL, glutamate cysteine ligase; GCLC, catalytic subunit of GCL; GPx, glutathione peroxidase; GR, glutathione reductase; GSH, reduced glutathione; GSSG, glutathione oxidized; H2O2, hydrogen peroxide; IEM, inborn errors of metabolism; Keratan sulfate; LPS, lipopolysaccharide; LSDs, lysosomal storage disorders; MPSs, mucopolysaccharidoses; Morquio A syndrome; Mucopolysaccharidosis type IVA; N-acetyl-galactosamine-6-sulfatase; OH•, hydroxyl radical; Oxidative stress; ROS, reactive oxygen species; SEM, standard error of the mean; SOD, superoxide dismutase; TLR4, Toll Like Receptor 4; TNB, tionitrobenzoic acid; mRNA, messenger ribonucleic acid