[A woman with a pure seminoma and a contralateral intratubular germinal neoplasm. A case report]. / Mujer con seminoma puro y neoplasia intratubular germinal contralateral. Informe de un caso.
Cir Cir
; 85(3): 245-249, 2017.
Article
em Es
| MEDLINE
| ID: mdl-26997294
BACKGROUND: Androgen insensitivity syndrome is an X-linked disorder, and is characterised by a female phenotype in a chromosomally male individual. It usually occurs in puberty with primary amenorrhoea or as an inguinal tumour in a female infant. In recent years, it is often also diagnosed in fertility clinics in adulthood. OBJECTIVE: The case is presented of a pure seminoma in a woman with the reference diagnosis of inguinal hernia. CLINICAL CASE: A 53 year old woman, who was operated on in 2014 due to a nodule in left groin. Androgen insensitivity syndrome was corroborated, and histopathology reported it as a right testicular seminoma. DISCUSSION: The importance of early diagnosis is discussed, highlighting the consequences of misdiagnosis, and question whether these patients have been adequately treated in the past. The risk of malignant transformation of an undescended testicle increases with age, thus gonadectomy should be performed after puberty, and in some cases hormone replacement therapy.
Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Síndrome de Resistência a Andrógenos
/
Neoplasias Testiculares
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Seminoma
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Criptorquidismo
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Disgenesia Gonadal 46 XY
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Neoplasias Primárias Múltiplas
Tipo de estudo:
Diagnostic_studies
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Etiology_studies
/
Screening_studies
Limite:
Female
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Humans
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Male
Idioma:
Es
Revista:
Cir Cir
Ano de publicação:
2017
Tipo de documento:
Article
País de publicação:
México