[Spinal abscess in a patient with hereditary hemorrhagic telangiectasia]. / Absceso intramedular en paciente con enfermedad de Rendu-Osler-Weber.
Medicina (B Aires)
; 67(6 Pt 2): 714-6, 2007.
Article
em Es
| MEDLINE
| ID: mdl-18422064
Rendu-Osler-Weber syndrome is an autosomal dominant disorder characterized by multiple skin and mucosal telangiectasis and multiorgan arteriovenous malformations. Neurological manifestations may occur because of cerebral arteriovenous malformations, intracranial hemorrhage, and most commonly by ischemic stroke and brain abscess secondary to paradoxical embolization in patients with pulmonary arteriovenous malformations. Intramedullary abscess is a rare, unusual condition, in Rendu-Osler-Weber syndrome. We report the case of a 56 years old woman, with a familial history of Rendu-Osler-Weber syndrome, admitted to intensive care with acute quadriplegia and hypoxemia. Our diagnosis was pulmonary arteriovenous malformations and intramedullary abscess.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Doenças da Coluna Vertebral
/
Telangiectasia Hemorrágica Hereditária
/
Fístula Arteriovenosa
/
Abscesso
Tipo de estudo:
Diagnostic_studies
Limite:
Female
/
Humans
/
Middle aged
Idioma:
Es
Revista:
Medicina (B Aires)
Ano de publicação:
2007
Tipo de documento:
Article
País de afiliação:
Argentina
País de publicação:
Argentina