Joubert syndrome. Respiratory failure requiring home mechanical ventilation.
Bol Asoc Med P R
; 83(10): 451-5, 1991 Oct.
Article
em En
| MEDLINE
| ID: mdl-1789891
A case of Joubert's Syndrome with respiratory insufficiency requiring mechanical ventilatory support is presented. The case illustrates the complex clinical, ethical and technical aspects in the management of patients with this syndrome and the feasibility of extending mechanical ventilatory support to the home setting. A caring, knowledgeable care team and a loving supportive family are required to properly continue treatment in the home in cases of this rare syndrome.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Respiração Artificial
/
Insuficiência Respiratória
/
Anormalidades Múltiplas
/
Serviços de Assistência Domiciliar
Tipo de estudo:
Diagnostic_studies
/
Etiology_studies
/
Guideline
Aspecto:
Ethics
/
Patient_preference
Limite:
Child, preschool
/
Humans
/
Male
Idioma:
En
Revista:
Bol Asoc Med P R
Ano de publicação:
1991
Tipo de documento:
Article
País de publicação:
Porto Rico