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[Fetal myelomeningocele and the potential in-utero repair: follow-up of 58 fetuses]. / Evolução de 58 fetos com meningomielocele e o potencial de reparo intra-útero.
Sbragia, Lourenço; Machado, Isabela Nelly; Rojas, Carlos Eduardo Braidos; Zambelli, Helder; Miranda, Márcio Lopes; Bianchi, Maria Otília; Barini, Ricardo.
Afiliação
  • Sbragia L; Faculdade de Ciências Médicas, Universidade Estadual de CampinasCampinas, SP, Brasil. sbragia@fcm.unicamp.br
Arq Neuropsiquiatr ; 62(2B): 487-91, 2004 Jun.
Article em Pt | MEDLINE | ID: mdl-15273849
INTRODUCTION: Prenatal diagnosis of myelomeningocele (MM) allows planning its management and, recently, a possible in utero repair. OBJECTIVE: To describe the perinatal outcome of fetuses with MM, in a Fetal Medicine Unit, identifying possible candidates for the in utero surgical repair. METHOD: Retrospective and descriptive study of 58 cases of prenatally diagnosed MM, at CAISM-UNICAMP, from January 1997 to December 2001, identifying possible fetal candidates for in utero repair. RESULTS: the diagnosis mean gestational age was 29 weeks (17-39); level of lesions was above sacral region in 85%, association with hydrocephaly in 86%. Surgical complications were present in 39% of the neonates. During follow-up, 98% presented neurogenic bladder and 60% neurological/mental handicap. Twenty eight fetuses (42%) could have indication of in utero repair. CONCLUSION: MM is associated with severe and frequent poor results. Almost one third of our cases could had fetal repair as a treatment choice.
Assuntos
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Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Meningomielocele / Doenças Fetais Tipo de estudo: Diagnostic_studies / Observational_studies / Prognostic_studies / Risk_factors_studies Limite: Adolescent / Adult / Female / Humans / Pregnancy Idioma: Pt Revista: Arq Neuropsiquiatr Ano de publicação: 2004 Tipo de documento: Article País de afiliação: Brasil País de publicação: Alemanha
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Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Meningomielocele / Doenças Fetais Tipo de estudo: Diagnostic_studies / Observational_studies / Prognostic_studies / Risk_factors_studies Limite: Adolescent / Adult / Female / Humans / Pregnancy Idioma: Pt Revista: Arq Neuropsiquiatr Ano de publicação: 2004 Tipo de documento: Article País de afiliação: Brasil País de publicação: Alemanha