Acute leukemia with natural killer cells antigens in Brazilian children.
Leuk Lymphoma
; 45(4): 739-43, 2004 Apr.
Article
em En
| MEDLINE
| ID: mdl-15160949
Malignancies arising from Natural Killer cells (NK) were described mainly comprising disorders related to large granular lymphocyte expansion. Clinical, morphological and immunophenotypic characteristics of myeloid/NK cell precursor acute leukemia (M/NK-AL) have been mainly described in adult patients. We identified nine children with M/NK-AL precursor cells in a series of 264 childhood acute leukemia diagnosed in our laboratory from consecutive referrals before treatment. CD34 +/-, CD13/33 +, CD11b +, a-MPO + and CD56 +, characterized these cases with TcR alphabeta and gammadelta negative cells. The differential diagnosis between subtypes of NK leukemia with those of lymphoid or myeloid origin in childhood raises the question regarding the pathogenesis and therapeutic implications of this rare entity in children.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Células Matadoras Naturais
/
Leucemia
Tipo de estudo:
Diagnostic_studies
/
Prognostic_studies
Limite:
Adolescent
/
Child
/
Child, preschool
/
Female
/
Humans
/
Male
País/Região como assunto:
America do sul
/
Brasil
Idioma:
En
Revista:
Leuk Lymphoma
Assunto da revista:
HEMATOLOGIA
/
NEOPLASIAS
Ano de publicação:
2004
Tipo de documento:
Article
País de afiliação:
Brasil
País de publicação:
Estados Unidos