Fibromatosis mesentérica: reporte de un caso / Mesenteric fibromatosis: report of one case
Rev. chil. cir
; 60(6): 557-560, dic. 2008. ilus
Article
em Es
| LILACS
| ID: lil-512409
Biblioteca responsável:
CL1.1
RESUMEN
El Tumor Desmolde o Fibromatosis Mesentérica es una enfermedad infrecuente en la que se reconocen 2 formas una esporádica y otra asociada a poliposis familiar adenomatosa. De etiología desconocida, su diagnóstico preoperatorio es dificultoso y el tratamiento de elección es quirúrgico. Se pone en consideración un caso de esta entidad en un varón joven, que se presentó con dolor abdominal y fiebre. Se realizó cirugía resectiva agresiva, otorgándose el alta a los 18 días de la intervención.
ABSTRACT
Desmoid tumor or mesenteric fibromatosis is an uncommon disease with to variants a sporadic form and one associated to familial adenomatous polyposis. Surgery is the treatment of choice. We report a 45 years old male presenting with abdominal pain and fever. An abdominal ultrasound informed the presence of a mass in the periumblical area. An Abdominal CAT sean showed a 13 cm diameter solid mass located in the left upper quadrant. The patient was operated and that mass is excised, requiring also a hemicolectomy, excision of the fourth portion of the duodenum and cholecystectomy. The pathology report of the excised tumor informs a mesenteric fibromatosis. The patient was discharged at the 18th postoperative day.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
LILACS
Assunto principal:
Neoplasias Peritoneais
/
Fibromatose Abdominal
/
Mesentério
Tipo de estudo:
Etiology_studies
Limite:
Humans
/
Male
Idioma:
Es
Revista:
Rev. chil. cir
Assunto da revista:
CIRURGIA GERAL
Ano de publicação:
2008
Tipo de documento:
Article
País de afiliação:
Argentina
País de publicação:
Chile