Research progress of cystic fibrosis associated Pseudo-Bartter syndrome / 中华实用儿科临床杂志
Chinese Journal of Applied Clinical Pediatrics
; (24): 1727-1729, 2022.
Article
en Zh
| WPRIM
| ID: wpr-954823
Biblioteca responsable:
WPRO
ABSTRACT
Cystic fibrosis (CF) is an autosomal recessive inherited disease affecting multiple body systems.Pseudo-Bartter syndrome (PBS) is a common manifestation of CF, with such clinical features as hypochloremia, hyponatremia, hypokalemia and metabolic alkalosis.However, PBS patients do not have renal tubulopathy.Children with CF are prone to develop electrolyte abnormalities due to fluid and electrolyte loss.In this article, the pathogenesis, clinical manifestations, diagnosis, and treatment of CF associated PBS were reviewed in order to enhance clinical understan-ding of this disease.
Texto completo:
1
Base de datos:
WPRIM
Idioma:
Zh
Revista:
Chinese Journal of Applied Clinical Pediatrics
Año:
2022
Tipo del documento:
Article