Non-IgG4-Related Fibrosclerosing Periaortitis with Multisystemic Involvement / 대한내과학회지
Korean Journal of Medicine
; : 749-754, 2014.
Article
en Ko
| WPRIM
| ID: wpr-85489
Biblioteca responsable:
WPRO
ABSTRACT
Fibrosclerosing periaortitis is a rare condition that refers to a spectrum of idiopathic diseases characterized by a fibroinflammatory reaction that extends from the adventitia of the aorta into the surrounding structures. It can be present in either IgG4-related or non-IgG4-related fibrosclerosing periaortitis. IgG4-related fibrosclerosing periaortitis could be associated with concomitant multi-organ involvement. However, non-IgG4-related fibrosclerosing periaortitis has rarely been associated with systemic manifestations. Here, we report a 76-year-old female with non-IgG4-related fibrosclerosing periaortitis, who developed pancytopenia, pleural effusion and ascites, which improved after high dose steroid treatment.
Palabras clave
Texto completo:
1
Base de datos:
WPRIM
Asunto principal:
Aorta
/
Pancitopenia
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Derrame Pleural
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Ascitis
/
Fibrosis Retroperitoneal
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Inmunoglobulina G
/
Adventicia
Límite:
Aged
/
Female
/
Humans
Idioma:
Ko
Revista:
Korean Journal of Medicine
Año:
2014
Tipo del documento:
Article