Severe Rhabdomyolysis in Phacomatosis Pigmentovascularis Type IIb associated with Sturge-Weber Syndrome / 대한중환자의학회지
Korean Journal of Critical Care Medicine
; : 329-335, 2015.
Article
en En
| WPRIM
| ID: wpr-25373
Biblioteca responsable:
WPRO
ABSTRACT
Phacomatosis pigmentovascularis (PPV) is a rare syndrome characterized by concurrent nevus flammeus (capillary malformation) and pigmentary nevus. According to current research, the major pathophysiologic mechanism in PPV is venous dysplasia with resultant compensatory collateral channels and venous hypertension. Arterial involvement is rare. We herein report our experience on renovascular hypertension, intermittent claudication, and severe rhabdomyolysis due to diffuse stenosis of multiple arteries in a patient with PPV type IIb associated with SWS.
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Texto completo:
1
Base de datos:
WPRIM
Asunto principal:
Arterias
/
Rabdomiólisis
/
Enfermedades Vasculares
/
Síndrome de Sturge-Weber
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Aneurisma Intracraneal
/
Constricción Patológica
/
Mancha Vino de Oporto
/
Síndromes Neurocutáneos
/
Hipertensión
/
Hipertensión Renovascular
Límite:
Humans
Idioma:
En
Revista:
Korean Journal of Critical Care Medicine
Año:
2015
Tipo del documento:
Article