Thromboembolic pulmonary hypertension due to disseminated fibromuscular dysplasia.
Pediatr Cardiol
; 17(5): 340-5, 1996.
Article
en En
| MEDLINE
| ID: mdl-8660454
We present two patients with thromboembolic pulmonary hypertension associated with unusual complications probably caused by disseminated fibromuscular dysplasia (FMD) or FMD-like vascular lesions. Intimal fibroplasia, which is typical of the vascular lesions associated with FMD, was observed in both patients. The presence of such intimal lesions suggests that there was a systemic factor that caused the formation of recurrent thrombi in the systemic vessels in these patients. These cases are the first ones reported in which an association between FMD and pulmonary hypertension has been observed. The pathogenesis of the thrombi in our patients was thought to be recurrent pulmonary thromboembolisms resulting from FMD.
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Colección:
01-internacional
Base de datos:
MEDLINE
Asunto principal:
Tromboembolia
/
Displasia Fibromuscular
/
Hipertensión Pulmonar
Tipo de estudio:
Diagnostic_studies
Límite:
Adolescent
/
Child
/
Female
/
Humans
/
Male
Idioma:
En
Revista:
Pediatr Cardiol
Año:
1996
Tipo del documento:
Article
País de afiliación:
Japón
Pais de publicación:
Estados Unidos