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Concurrent delayed recurrence of peripheral primitive neuroectodermal tumors in orbital and sellar/suprasellar regions in an older adult.
Yamashita, Shota; Yokosawa, Michiko; Ono, Sadahide; Sugawara, Takayuki; Kimura, Naoto; Endo, Hidenori.
Afiliación
  • Yamashita S; Department of Neurosurgery, Iwate Prefectural Central Hospital, Morioka, Japan.
  • Yokosawa M; Department of Neurosurgery, Iwate Prefectural Central Hospital, Morioka, Japan.
  • Ono S; Department of Pathology, Iwate Prefectural Central Hospital, Morioka, Japan.
  • Sugawara T; Department of Neurosurgery, Iwate Prefectural Central Hospital, Morioka, Japan.
  • Kimura N; Department of Neurosurgery, Iwate Prefectural Central Hospital, Morioka, Japan.
  • Endo H; Department of Neurosurgery, Tohoku University Graduate School of Medicine, Sendai, Japan.
Eur J Ophthalmol ; : 11206721241277251, 2024 Sep 03.
Article en En | MEDLINE | ID: mdl-39228192
ABSTRACT

BACKGROUND:

Peripheral primitive neuroectodermal tumors (pPNETs) are rare and aggressive small round cell tumors, tending to occur in the thoracic and paravertebral soft tissues in children and young adults. This report describes an exceptionally rare case of concurrent delayed recurrence of pPNET in the orbital and sellar/suprasellar regions in an older adult, with a discussion supported by a literature review. CASE PRESENTATION We report an 82-year-old woman with a history of orbital pPNETs resection at age 62, followed by gamma knife radiosurgery for local recurrence at age 66. She presented left eye pain, left eye protrusion, decreased vision in the right eye, and right homonymous hemianopia. MRI revealed extensive lesions in the left orbital cavity and sellar/suprasellar region, contiguous through the optic canal. The recurrent tumor was treated through a two-stage resection via transcranial and transsphenoidal approaches, which resulted in symptom improvement and a pathologic diagnosis of pPNETs.

CONCLUSION:

This case highlights a highly rare instance of late-onset orbital pPNETs recurrence in an elderly patient, with evidence suggesting tumor progression into the sellar/suprasellar regions through the optic canal.
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Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Idioma: En Revista: Eur J Ophthalmol Asunto de la revista: OFTALMOLOGIA Año: 2024 Tipo del documento: Article País de afiliación: Japón Pais de publicación: Estados Unidos
Texto completo
Añadir a Mi BVS
Imprimir
XML
PubMed Links
Buscar en Google

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Idioma: En Revista: Eur J Ophthalmol Asunto de la revista: OFTALMOLOGIA Año: 2024 Tipo del documento: Article País de afiliación: Japón Pais de publicación: Estados Unidos