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Granulomatosis With Polyangiitis: Cardiac, Renal, and Respiratory Involvement.
Khatiwala, Pooja; Patel, Parita; Nachodsky, Alexandria.
Afiliación
  • Khatiwala P; Internal Medicine, Cooper University Hospital, Camden, USA.
  • Patel P; Internal Medicine, Cooper University Hospital, Camden, USA.
  • Nachodsky A; Internal Medicine, Cooper University Hospital, Camden, USA.
Cureus ; 16(6): e61529, 2024 Jun.
Article en En | MEDLINE | ID: mdl-38957259
ABSTRACT
Granulomatosis with polyangiitis (GPA), formerly known as Wegener's granulomatosis, is an anti-neutrophilic cytoplasmic autoantibody (ANCA)-associated small-vessel vasculitis. Typically, it causes upper and lower respiratory tract necrotizing granulomatous inflammation and necrotizing glomerulonephritis. The diagnosis is made through clinical symptoms, positive antibody testing, imaging, and kidney biopsy. We describe the case of a man in his 60s who presented with multiple complications of GPA including rapidly progressive renal failure requiring dialysis, diffuse alveolar hemorrhage, acute respiratory distress syndrome (ARDS), circulatory shock, submassive pulmonary embolism, and biventricular and dilated cardiomyopathy.
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Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Idioma: En Revista: Cureus Año: 2024 Tipo del documento: Article País de afiliación: Estados Unidos Pais de publicación: Estados Unidos

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Idioma: En Revista: Cureus Año: 2024 Tipo del documento: Article País de afiliación: Estados Unidos Pais de publicación: Estados Unidos