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Two cases of airway-centered fibroelastosis treated with an antifibrotic agent and corticosteroids.
Kamatani, Miwa; Inomata, Minoru; Misumi, Akari; Ito, Ken; Maeda, Takashi; Chin, Haruka; Ito, Yu; Sakamoto, Keita; Awano, Nobuyasu; Kuse, Naoyuki; Furuhata, Yoshiaki; Bae, Yuan; Sugiura, Hiroaki; Takemura, Tamiko; Izumo, Takehiro.
Afiliación
  • Kamatani M; Department of Respiratory Medicine, Japanese Red Cross Medical Center, Japan.
  • Inomata M; Department of Respiratory Medicine, Japanese Red Cross Medical Center, Japan.
  • Misumi A; Department of Respiratory Medicine, Japanese Red Cross Medical Center, Japan.
  • Ito K; Department of Respiratory Medicine, Japanese Red Cross Medical Center, Japan.
  • Maeda T; Department of Respiratory Medicine, Japanese Red Cross Medical Center, Japan.
  • Chin H; Department of Respiratory Medicine, Japanese Red Cross Medical Center, Japan.
  • Ito Y; Department of Respiratory Medicine, Japanese Red Cross Medical Center, Japan.
  • Sakamoto K; Department of Respiratory Medicine, Japanese Red Cross Medical Center, Japan.
  • Awano N; Department of Respiratory Medicine, Japanese Red Cross Medical Center, Japan.
  • Kuse N; Department of Respiratory Medicine, Japanese Red Cross Medical Center, Japan.
  • Furuhata Y; Department of Respiratory Surgery, Japanese Red Cross Medical Center, Japan.
  • Bae Y; Department of Pathology, Japanese Red Cross Medical Center, Japan.
  • Sugiura H; Department of Radiology, National Defense Medical College Hospital, Japan.
  • Takemura T; Department of Pathology, Kanagawa Cardiovascular and Respiratory Center, Japan.
  • Izumo T; Department of Respiratory Medicine, Japanese Red Cross Medical Center, Japan.
Respir Med Case Rep ; 50: 102036, 2024.
Article en En | MEDLINE | ID: mdl-38812525
ABSTRACT
Airway-centered fibroelastosis is characterized by peribronchovascular fibroelastosis, predominantly in the upper lobes, with little-to-no pleural involvement. In this study, we describe two cases of airway-centered fibroelastosis diagnosed based on radiological and pathological findings. The first case comprised a 44-year-old man whose forced vital capacity improved over three months following treatment with nintedanib. The second case involved a 50-year-old woman who was treated with oral corticosteroids but yielded an unfavorable outcome. An effective treatment for airway-centered fibroelastosis has not yet been identified; therefore, this study may help contribute to a more thorough discussion regarding treatment strategies for this disease.
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Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Idioma: En Revista: Respir Med Case Rep Año: 2024 Tipo del documento: Article País de afiliación: Japón Pais de publicación: Reino Unido

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Idioma: En Revista: Respir Med Case Rep Año: 2024 Tipo del documento: Article País de afiliación: Japón Pais de publicación: Reino Unido