Uhl's Anomaly in Adulthood.
World J Pediatr Congenit Heart Surg
; 15(4): 523-525, 2024 Jul.
Article
en En
| MEDLINE
| ID: mdl-38693789
ABSTRACT
Uhl's anomaly is a rare congenital syndrome characterized by the absence of right ventricular myocardium. The widely accepted pathological mechanism is intrauterine myocardial apoptosis. Uhl's syndrome carries a poor prognosis. In rare situations, patients with Uhl's anomaly reach adulthood. We will present a case of a 29-year-old patient with Uhl's syndrome treated at our center, highlighting the diagnostic, surgical, and postoperative challenges in management.
Texto completo:
1
Colección:
01-internacional
Base de datos:
MEDLINE
Asunto principal:
Cardiopatías Congénitas
Límite:
Adult
/
Female
/
Humans
/
Male
Idioma:
En
Revista:
World J Pediatr Congenit Heart Surg
Año:
2024
Tipo del documento:
Article
País de afiliación:
Egipto
Pais de publicación:
Estados Unidos