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Arrhythmogenic Left Ventricular Cardiomyopathy: From Diagnosis to Risk Management.
Mauriello, Alfredo; Roma, Anna Selvaggia; Ascrizzi, Antonia; Molinari, Riccardo; Loffredo, Francesco S; D'Andrea, Antonello; Russo, Vincenzo.
Afiliación
  • Mauriello A; Cardiology Unit, Department of Medical Translational Science, University of Campania "Luigi Vanvitelli"-"V. Monaldi" Hospital, 80126 Naples, Italy.
  • Roma AS; Unit of Cardiology, "Umberto I" Hospital, 84014 Nocera Inferiore, Italy.
  • Ascrizzi A; Cardiology Unit, Department of Medical Translational Science, University of Campania "Luigi Vanvitelli"-"V. Monaldi" Hospital, 80126 Naples, Italy.
  • Molinari R; Cardiology Unit, Department of Medical Translational Science, University of Campania "Luigi Vanvitelli"-"V. Monaldi" Hospital, 80126 Naples, Italy.
  • Loffredo FS; Cardiology Unit, Department of Medical Translational Science, University of Campania "Luigi Vanvitelli"-"V. Monaldi" Hospital, 80126 Naples, Italy.
  • D'Andrea A; Cardiology Unit, Department of Medical Translational Science, University of Campania "Luigi Vanvitelli"-"V. Monaldi" Hospital, 80126 Naples, Italy.
  • Russo V; Cardiology Unit, Department of Medical Translational Science, University of Campania "Luigi Vanvitelli"-"V. Monaldi" Hospital, 80126 Naples, Italy.
J Clin Med ; 13(7)2024 Mar 22.
Article en En | MEDLINE | ID: mdl-38610600
ABSTRACT
PURPOSE OF REVIEW Left ventricular arrhythmogenic cardiomyopathy (ALVC) is a rare and poorly characterized cardiomyopathy that has recently been reclassified in the group of non-dilated left ventricular cardiomyopathies. This review aims to summarize the background, diagnosis, and sudden cardiac death risk in patients presenting this cardiomyopathy. RECENT

FINDINGS:

Although there is currently a lack of data on this condition, arrhythmogenic left ventricular dysplasia can be considered a specific disease of the left ventricle (LV). We have collected the latest evidence about the management and the risks associated with this cardiomyopathy.

SUMMARY:

Left ventricular arrhythmogenic cardiomyopathy is still poorly characterized. ALVC is characterized by fibrofatty replacement in the left ventricular myocardium, with variable phenotypic expression. Diagnosis is based on a multiparametric approach, including cardiac magnetic resonance (CMR) and genetic testing, and is important for sudden cardiac death (SCD) risk stratification and management. Recent guidelines have improved the management of left ventricular arrhythmogenic cardiomyopathy. Further studies are necessary to improve knowledge of this cardiomyopathy.
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Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Idioma: En Revista: J Clin Med Año: 2024 Tipo del documento: Article País de afiliación: Italia Pais de publicación: Suiza

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Idioma: En Revista: J Clin Med Año: 2024 Tipo del documento: Article País de afiliación: Italia Pais de publicación: Suiza