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Long-term safety, tolerability, and efficacy of efgartigimod (ADAPT+): interim results from a phase 3 open-label extension study in participants with generalized myasthenia gravis.
Howard, James F; Bril, Vera; Vu, Tuan; Karam, Chafic; Peric, Stojan; De Bleecker, Jan L; Murai, Hiroyuki; Meisel, Andreas; Beydoun, Said R; Pasnoor, Mamatha; Guglietta, Antonio; Van Hoorick, Benjamin; Steeland, Sophie; T'joen, Caroline; Utsugisawa, Kimiaki; Verschuuren, Jan; Mantegazza, Renato.
Afiliación
  • Howard JF; Department of Neurology, The University of North Carolina at Chapel Hill, Chapel Hill, NC, United States.
  • Bril V; Ellen and Martin Prosserman Centre for Neuromuscular Diseases, University Health Network, University of Toronto, Toronto, ON, Canada.
  • Vu T; Department of Neurology, University of South Florida Morsani College of Medicine, Tampa, FL, United States.
  • Karam C; Penn Neuroscience Center-Neurology, Hospital of the University of Pennsylvania, Philadelphia, PA, United States.
  • Peric S; Neurology Clinic, University Clinical Center of Serbia, Faculty of Medicine, University of Belgrade, Belgrade, Serbia.
  • De Bleecker JL; Department of Neurology and Neuromuscular Reference Center, Ghent University Hospital, Ghent, Belgium.
  • Murai H; Department of Neurology, School of Medicine, International University of Health and Welfare, Narita, Japan.
  • Meisel A; Department of Neurology, Charité - Universitätsmedizin Berlin, Berlin, Germany.
  • Beydoun SR; Department of Neurology, Keck School of Medicine, University of Southern California, Los Angeles, CA, United States.
  • Pasnoor M; Department of Neurology, University of Kansas Medical Center, Kansas City, KS, United States.
  • Guglietta A; argenx, Ghent, Belgium.
  • Van Hoorick B; argenx, Ghent, Belgium.
  • Steeland S; argenx, Ghent, Belgium.
  • T'joen C; argenx, Ghent, Belgium.
  • Utsugisawa K; Department of Neurology, Hanamaki General Hospital, Hanamaki, Japan.
  • Verschuuren J; Department of Neurology, Leiden University Medical Center, Leiden, Netherlands.
  • Mantegazza R; Department of Neuroimmunology and Neuromuscular Diseases, Fondazione Istituto Carlo Besta, Milan, Italy.
Front Neurol ; 14: 1284444, 2023.
Article en En | MEDLINE | ID: mdl-38318236
ABSTRACT

Objective:

ADAPT+ assessed the long-term safety, tolerability, and efficacy of efgartigimod in adult participants with generalized myasthenia gravis (gMG).

Methods:

ADAPT+ was an open-label, single-arm, multicenter, up to 3-year extension of the pivotal phase 3 ADAPT study. Efgartigimod was administered in treatment cycles of 4 intravenous infusions (one 10 mg/kg infusion per week). Initiation of subsequent treatment cycles was individualized based on clinical evaluation. Safety endpoints included incidence and severity of adverse events. Efficacy endpoints assessed disease severity using Myasthenia Gravis-Activities of Daily Living (MG-ADL) and Quantitative Myasthenia Gravis (QMG) scores.

Results:

As of January 2022, 151 participants had rolled over to ADAPT+ and 145 had received ≥1 dose of efgartigimod, of whom, 111 (76.6%) were AChR-Ab+ and 34 (23.4%) were AChR-Ab-. Mean study duration (treatment plus follow-up) was 548 days, and participants received up to 17 treatment cycles, corresponding to 217.6 participant-years of exposure. In the overall population, 123 (84.8%) participants reported ≥1 treatment-emergent adverse event; most frequent were headache (36 [24.8%]), COVID-19 (22 [15.2%]), and nasopharyngitis (20 [13.8%]). Clinically meaningful improvement (CMI) in mean MG-ADL and QMG scores was seen as early as 1 week following the first infusion across multiple cycles in AChR-Ab+ and AChR-Ab- participants. Maximal MG-ADL and QMG improvements aligned with onset and magnitude of total IgG and AChR-Ab reductions. For AChR-Ab+ participants at any time point in each of the first 10 treatment cycles, more than 90% had a maximum reduction of ≥2 points (CMI) in MG-ADL total score; across the 7 cycles in which QMG was measured, 69.4% to 91.3% of participants demonstrated a maximum reduction of ≥3 points (CMI) in QMG total score. Many participants demonstrated improvements well beyond CMI thresholds. In AChR-Ab+ participants with ≥1 year of combined follow-up between ADAPT and ADAPT+, mean number of annualized cycles was 4.7 per year (median [range] 5.0 [0.5-7.6]).

Conclusion:

Results of ADAPT+ corroborate the substantial clinical improvements seen with efgartigimod in ADAPT and support its long-term safety, tolerability, and efficacy, as well as an individualized dosing regimen for treatment of gMG. Clinical trial registration https//classic.clinicaltrials.gov/ct2/show/NCT03770403, NCT03770403.
Palabras clave

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Tipo de estudio: Clinical_trials Idioma: En Revista: Front Neurol Año: 2023 Tipo del documento: Article País de afiliación: Estados Unidos Pais de publicación: Suiza

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Tipo de estudio: Clinical_trials Idioma: En Revista: Front Neurol Año: 2023 Tipo del documento: Article País de afiliación: Estados Unidos Pais de publicación: Suiza