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Idiopathic and connective tissue disease-associated pulmonary arterial hypertension (PAH): Similarities, differences and the role of autoimmunity.
Favoino, Elvira; Prete, Marcella; Liakouli, Vasiliki; Leone, Patrizia; Sisto, Adriana; Navarini, Luca; Vomero, Marta; Ciccia, Francesco; Ruscitti, Piero; Racanelli, Vito; Giacomelli, Roberto; Perosa, Federico.
Afiliación
  • Favoino E; Laboratory of Cellular and Molecular Immunology, Department of Interdisciplinary Medicine, University of Bari Medical School, Bari, Italy. Electronic address: elvira.favoino@uniba.it.
  • Prete M; Internal Medicine Unit, Department of Interdisciplinary Medicine, University of Bari Medical School, Bari, Italy.
  • Liakouli V; Rheumatology Section, Department of Precision Medicine, University of Campania "Luigi Vanvitelli", Naples, Italy.
  • Leone P; Internal Medicine Unit, Department of Interdisciplinary Medicine, University of Bari Medical School, Bari, Italy.
  • Sisto A; Rheumatic and Systemic Autoimmune Diseases Unit, Department of Interdisciplinary Medicine, University of Bari Medical School, Bari, Italy.
  • Navarini L; Clinical and research section of Rheumatology and Clinical Immunology, Fondazione Policlinico Campus Bio-Medico, Via Álvaro del Portillo 200, 00128, Rome, Italy; Rheumatology and Clinical Immunology, Department of Medicine, University of Rome "Campus Biomedico", School of Medicine, Rome, Italy.
  • Vomero M; Clinical and research section of Rheumatology and Clinical Immunology, Fondazione Policlinico Campus Bio-Medico, Via Álvaro del Portillo 200, 00128, Rome, Italy; Rheumatology and Clinical Immunology, Department of Medicine, University of Rome "Campus Biomedico", School of Medicine, Rome, Italy.
  • Ciccia F; Rheumatology Section, Department of Precision Medicine, University of Campania "Luigi Vanvitelli", Naples, Italy.
  • Ruscitti P; Rheumatology Unit, Department of Biotechnological and Applied Clinical Sciences, University of L'Aquila, L'Aquila, Italy.
  • Racanelli V; Centre for Medical Sciences, University of Trento and Internal Medicine Division, Santa Chiara Hospital, Provincial Health Care Agency (APSS), Trento, Italy.
  • Giacomelli R; Clinical and research section of Rheumatology and Clinical Immunology, Fondazione Policlinico Campus Bio-Medico, Via Álvaro del Portillo 200, 00128, Rome, Italy; Rheumatology and Clinical Immunology, Department of Medicine, University of Rome "Campus Biomedico", School of Medicine, Rome, Italy.
  • Perosa F; Rheumatic and Systemic Autoimmune Diseases Unit, Department of Interdisciplinary Medicine, University of Bari Medical School, Bari, Italy. Electronic address: federico.perosa@uniba.it.
Autoimmun Rev ; 23(4): 103514, 2024 Apr.
Article en En | MEDLINE | ID: mdl-38181859
ABSTRACT
Pre-capillary pulmonary arterial hypertension (PAH) is hemodynamically characterized by a mean pulmonary arterial pressure (mPAP) ≥ 20 mmHg, pulmonary capillary wedge pressure (PAWP) ≤15 mmHg and pulmonary vascular resistance (PVR) > 2. PAH is classified in six clinical subgroups, including idiopathic PAH (IPAH) and PAH associated to connective tissue diseases (CTD-PAH), that will be the main object of this review. The aim is to compare these two PAH subgroups in terms of epidemiology, histological and pathogenic findings in an attempt to define disease-specific features, including autoimmunity, that may explain the heterogeneity of response to therapy between IPAH and CTD-PAH.
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Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Autoinmunidad / Enfermedades del Tejido Conjuntivo Tipo de estudio: Risk_factors_studies Límite: Humans Idioma: En Revista: Autoimmun Rev Asunto de la revista: ALERGIA E IMUNOLOGIA Año: 2024 Tipo del documento: Article Pais de publicación: Países Bajos
Texto completo
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Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Autoinmunidad / Enfermedades del Tejido Conjuntivo Tipo de estudio: Risk_factors_studies Límite: Humans Idioma: En Revista: Autoimmun Rev Asunto de la revista: ALERGIA E IMUNOLOGIA Año: 2024 Tipo del documento: Article Pais de publicación: Países Bajos