Glutamine energy substrate anaplerosis increases bone density in the Pah<sup>enu2</sup> classical PKU mouse in the absence of phenylalanine restriction.

Dobrowolski, Steven F; Phua, Yu Leng; Tourkova, Irina L; Sudano, Cayla; Vockley, Jerry; Larrouture, Quitterie C; Blair, Harry C

Glutamine energy substrate anaplerosis increases bone density in the Pah^enu2 classical PKU mouse in the absence of phenylalanine restriction.

Dobrowolski, Steven F; Phua, Yu Leng; Tourkova, Irina L; Sudano, Cayla; Vockley, Jerry; Larrouture, Quitterie C; Blair, Harry C.

Afiliación

Dobrowolski SF; Department of Pathology University of Pittsburgh, School of Medicine Pittsburgh Pennsylvania USA.
Phua YL; Division of Medical Genetics and Genomics Children's Hospital of Pittsburgh Pittsburgh Pennsylvania USA.
Tourkova IL; Present address: Department of Genetics and Genomic Sciences Icahn School of Medicine at Mount Sinai New York USA.
Sudano C; Department of Pathology University of Pittsburgh, School of Medicine Pittsburgh Pennsylvania USA.
Vockley J; Pittsburgh Veteran's Affairs Medical Center Pittsburgh Pennsylvania USA.
Larrouture QC; Department of Pathology University of Pittsburgh, School of Medicine Pittsburgh Pennsylvania USA.
Blair HC; Division of Medical Genetics and Genomics Children's Hospital of Pittsburgh Pittsburgh Pennsylvania USA.

JIMD Rep ; 63(5): 446-452, 2022 Sep.

Article en En | MEDLINE | ID: mdl-36101821

Palabras clave

Pahenu2; glutamine; osteopenia; oxidative phosphorylation; phenylketonuria

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Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Idioma: En Revista: JIMD Rep Año: 2022 Tipo del documento: Article Pais de publicación: Estados Unidos

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