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Metabolic Control and "Ideal" Outcomes in Liver Transplantation for Maple Syrup Urine Disease.
Ewing, Caroline B; Soltys, Kyle A; Strauss, Kevin A; Sindhi, Rakesh; Vockley, Jerry; McKiernan, Patrick; Squires, Robert H; Bond, Geoffrey; Ganoza, Armando; Khanna, Ajai; Mazariegos, George V; Squires, James E.
Afiliación
  • Ewing CB; University of Pittsburgh School of Medicine, Pittsburgh, PA.
  • Soltys KA; Thomas E. Starzl Transplantation Institute, Hillman Center for Pediatric Transplantation, Department of Transplant Surgery, University of Pittsburgh Medical Center (UPMC) Children's Hospital of Pittsburgh, Pittsburgh, PA.
  • Strauss KA; Clinic for Special Children, Strasburg, PA.
  • Sindhi R; Thomas E. Starzl Transplantation Institute, Hillman Center for Pediatric Transplantation, Department of Transplant Surgery, University of Pittsburgh Medical Center (UPMC) Children's Hospital of Pittsburgh, Pittsburgh, PA.
  • Vockley J; Center for Rare Disease Therapy, University of Pittsburgh Medical Center (UPMC) Children's Hospital of Pittsburgh, Pittsburgh, PA.
  • McKiernan P; Division of Gastroenterology, Hepatology, and Nutrition, University of Pittsburgh Medical Center (UPMC) Children's Hospital of Pittsburgh, Pittsburgh, PA.
  • Squires RH; Division of Gastroenterology, Hepatology, and Nutrition, University of Pittsburgh Medical Center (UPMC) Children's Hospital of Pittsburgh, Pittsburgh, PA.
  • Bond G; Thomas E. Starzl Transplantation Institute, Hillman Center for Pediatric Transplantation, Department of Transplant Surgery, University of Pittsburgh Medical Center (UPMC) Children's Hospital of Pittsburgh, Pittsburgh, PA.
  • Ganoza A; Thomas E. Starzl Transplantation Institute, Hillman Center for Pediatric Transplantation, Department of Transplant Surgery, University of Pittsburgh Medical Center (UPMC) Children's Hospital of Pittsburgh, Pittsburgh, PA.
  • Khanna A; Thomas E. Starzl Transplantation Institute, Hillman Center for Pediatric Transplantation, Department of Transplant Surgery, University of Pittsburgh Medical Center (UPMC) Children's Hospital of Pittsburgh, Pittsburgh, PA.
  • Mazariegos GV; Thomas E. Starzl Transplantation Institute, Hillman Center for Pediatric Transplantation, Department of Transplant Surgery, University of Pittsburgh Medical Center (UPMC) Children's Hospital of Pittsburgh, Pittsburgh, PA.
  • Squires JE; Division of Gastroenterology, Hepatology, and Nutrition, University of Pittsburgh Medical Center (UPMC) Children's Hospital of Pittsburgh, Pittsburgh, PA. Electronic address: James.Squires2@chp.edu.
J Pediatr ; 237: 59-64.e1, 2021 Oct.
Article en En | MEDLINE | ID: mdl-34153280

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Trasplante de Hígado / Aminoácidos de Cadena Ramificada / Enfermedad de la Orina de Jarabe de Arce Tipo de estudio: Diagnostic_studies / Observational_studies / Prognostic_studies / Risk_factors_studies Límite: Adolescent / Adult / Child / Child, preschool / Female / Humans / Infant / Male Idioma: En Revista: J Pediatr Año: 2021 Tipo del documento: Article País de afiliación: Panamá Pais de publicación: Estados Unidos

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Trasplante de Hígado / Aminoácidos de Cadena Ramificada / Enfermedad de la Orina de Jarabe de Arce Tipo de estudio: Diagnostic_studies / Observational_studies / Prognostic_studies / Risk_factors_studies Límite: Adolescent / Adult / Child / Child, preschool / Female / Humans / Infant / Male Idioma: En Revista: J Pediatr Año: 2021 Tipo del documento: Article País de afiliación: Panamá Pais de publicación: Estados Unidos