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Impaired Binding to Junctophilin-2 and Nanostructural Alteration in CPVT Mutation.
Yin, Liheng; Zahradnikova, Alexandra; Rizzetto, Riccardo; Boncompagni, Simona; Rabesahala de Meritens, Camille; Zhang, Yadan; Joanne, Pierre; Marqués-Sulé, Elena; Aguilar-Sánchez, Yuriana; Fernández-Tenorio, Miguel; Villejoubert, Olivier; Li, Linwei; Wang, Yue Yi; Mateo, Philippe; Nicolas, Valérie; Gerbaud, Pascale; Lai, F Anthony; Perrier, Romain; Álvarez, Julio L; Niggli, Ernst; Valdivia, Héctor H; Valdivia, Carmen R; Ramos-Franco, Josefina; Zorio, Esther; Zissimopoulos, Spyros; Protasi, Feliciano; Benitah, Jean-Pierre; Gómez, Ana M.
Afiliación
  • Yin L; Signaling and Cardiovascular Pathophysiology - UMR-S 1180, Inserm, Université Paris-Saclay 92296 Châtenay-Malabry, France (L.Y., A.Z., R.R., P.J., E.M.-S., O.V., L.L., Y.Y.W., P.M., P.G., R.P., J.L.A., J.-P.B., A.M.G.).
  • Zahradnikova A; Signaling and Cardiovascular Pathophysiology - UMR-S 1180, Inserm, Université Paris-Saclay 92296 Châtenay-Malabry, France (L.Y., A.Z., R.R., P.J., E.M.-S., O.V., L.L., Y.Y.W., P.M., P.G., R.P., J.L.A., J.-P.B., A.M.G.).
  • Rizzetto R; Signaling and Cardiovascular Pathophysiology - UMR-S 1180, Inserm, Université Paris-Saclay 92296 Châtenay-Malabry, France (L.Y., A.Z., R.R., P.J., E.M.-S., O.V., L.L., Y.Y.W., P.M., P.G., R.P., J.L.A., J.-P.B., A.M.G.).
  • Boncompagni S; CAST, Department of Neuroscience, Imaging and Clinical Sciences (DNICS), Medicine and Ageing Sciences (DMSI), University Gabriele d'Annunzio, Chieti, Italy (S.B., F.P.).
  • Rabesahala de Meritens C; Swansea University Medical School, Institute of Life Science, Swansea, SA2 8PP, UK (C.R.d.M., Y.Z., S.Z.).
  • Zhang Y; Swansea University Medical School, Institute of Life Science, Swansea, SA2 8PP, UK (C.R.d.M., Y.Z., S.Z.).
  • Joanne P; Signaling and Cardiovascular Pathophysiology - UMR-S 1180, Inserm, Université Paris-Saclay 92296 Châtenay-Malabry, France (L.Y., A.Z., R.R., P.J., E.M.-S., O.V., L.L., Y.Y.W., P.M., P.G., R.P., J.L.A., J.-P.B., A.M.G.).
  • Marqués-Sulé E; Signaling and Cardiovascular Pathophysiology - UMR-S 1180, Inserm, Université Paris-Saclay 92296 Châtenay-Malabry, France (L.Y., A.Z., R.R., P.J., E.M.-S., O.V., L.L., Y.Y.W., P.M., P.G., R.P., J.L.A., J.-P.B., A.M.G.).
  • Aguilar-Sánchez Y; Physiotherapy, University of Valencia, Valencia, Spain (E.M.-S.).
  • Fernández-Tenorio M; Physiology and Biophysics, Rush University Medical Center, Chicago, IL, USA (Y.A.-S., J.R.-F.).
  • Villejoubert O; Physiology, University of Bern, Bern, Switzerland (M.F.-T., E.N.).
  • Li L; Signaling and Cardiovascular Pathophysiology - UMR-S 1180, Inserm, Université Paris-Saclay 92296 Châtenay-Malabry, France (L.Y., A.Z., R.R., P.J., E.M.-S., O.V., L.L., Y.Y.W., P.M., P.G., R.P., J.L.A., J.-P.B., A.M.G.).
  • Wang YY; Signaling and Cardiovascular Pathophysiology - UMR-S 1180, Inserm, Université Paris-Saclay 92296 Châtenay-Malabry, France (L.Y., A.Z., R.R., P.J., E.M.-S., O.V., L.L., Y.Y.W., P.M., P.G., R.P., J.L.A., J.-P.B., A.M.G.).
  • Mateo P; Signaling and Cardiovascular Pathophysiology - UMR-S 1180, Inserm, Université Paris-Saclay 92296 Châtenay-Malabry, France (L.Y., A.Z., R.R., P.J., E.M.-S., O.V., L.L., Y.Y.W., P.M., P.G., R.P., J.L.A., J.-P.B., A.M.G.).
  • Nicolas V; Signaling and Cardiovascular Pathophysiology - UMR-S 1180, Inserm, Université Paris-Saclay 92296 Châtenay-Malabry, France (L.Y., A.Z., R.R., P.J., E.M.-S., O.V., L.L., Y.Y.W., P.M., P.G., R.P., J.L.A., J.-P.B., A.M.G.).
  • Gerbaud P; IPSIT, 92296 Châtenay-Malabry, France (V.N.).
  • Lai FA; Signaling and Cardiovascular Pathophysiology - UMR-S 1180, Inserm, Université Paris-Saclay 92296 Châtenay-Malabry, France (L.Y., A.Z., R.R., P.J., E.M.-S., O.V., L.L., Y.Y.W., P.M., P.G., R.P., J.L.A., J.-P.B., A.M.G.).
  • Perrier R; College of Medicine, Biomedical & Pharmaceutical Research Unit, QU Health, & Biomedical Research Centre, Qatar University, Doha, Qatar (F.A.L.).
  • Niggli E; Signaling and Cardiovascular Pathophysiology - UMR-S 1180, Inserm, Université Paris-Saclay 92296 Châtenay-Malabry, France (L.Y., A.Z., R.R., P.J., E.M.-S., O.V., L.L., Y.Y.W., P.M., P.G., R.P., J.L.A., J.-P.B., A.M.G.).
  • Valdivia HH; Institute of Cardiology, Havana, Cuba (J.L.A.).
  • Valdivia CR; Physiology, University of Bern, Bern, Switzerland (M.F.-T., E.N.).
  • Ramos-Franco J; Medicine and Cardiovascular Research Center, University of Wisconsin-Madison School of Medicine and Public Health, Madison, Wisconsin (H.H.V., C.R.V.).
  • Zorio E; Medicine and Cardiovascular Research Center, University of Wisconsin-Madison School of Medicine and Public Health, Madison, Wisconsin (H.H.V., C.R.V.).
  • Zissimopoulos S; Physiology and Biophysics, Rush University Medical Center, Chicago, IL, USA (Y.A.-S., J.R.-F.).
  • Protasi F; Cardiology Department and Unidad de Cardiopatías Familiares, Muerte Súbita y Mecanismos de Enfermedad (CaFaMuSMe), Hospital Universitario y Politécnico La Fe and Instituto de Investigación Sanitaria La Fe, Valencia, Spain (E.Z.).
  • Benitah JP; Center for Biomedical Network Research on Cardiovascular diseases (CIBERCV), Madrid, Spain (E.Z.).
  • Gómez AM; Swansea University Medical School, Institute of Life Science, Swansea, SA2 8PP, UK (C.R.d.M., Y.Z., S.Z.).
Circ Res ; 129(3): e35-e52, 2021 07 23.
Article en En | MEDLINE | ID: mdl-34111951

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Taquicardia Ventricular / Canal Liberador de Calcio Receptor de Rianodina / Señalización del Calcio / Miocitos Cardíacos / Proteínas de la Membrana Límite: Animals / Humans Idioma: En Revista: Circ Res Año: 2021 Tipo del documento: Article Pais de publicación: Estados Unidos

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Taquicardia Ventricular / Canal Liberador de Calcio Receptor de Rianodina / Señalización del Calcio / Miocitos Cardíacos / Proteínas de la Membrana Límite: Animals / Humans Idioma: En Revista: Circ Res Año: 2021 Tipo del documento: Article Pais de publicación: Estados Unidos