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Low human dystrophin levels prevent cardiac electrophysiological and structural remodelling in a Duchenne mouse model.
Marchal, Gerard A; van Putten, Maaike; Verkerk, Arie O; Casini, Simona; Putker, Kayleigh; van Amersfoorth, Shirley C M; Aartsma-Rus, Annemieke; Lodder, Elisabeth M; Remme, Carol Ann.
Afiliación
  • Marchal GA; Department of Experimental Cardiology, Amsterdam UMC (Location AMC), Meibergdreef 9, 1005 AZ, Amsterdam, The Netherlands. g.a.marchal@amsterdamumc.nl.
  • van Putten M; Department of Human Genetics, Leiden University Medical Center, Albinusdreef 2, 2333 ZA, Leiden, The Netherlands.
  • Verkerk AO; Department of Experimental Cardiology, Amsterdam UMC (Location AMC), Meibergdreef 9, 1005 AZ, Amsterdam, The Netherlands.
  • Casini S; Amsterdam UMC (Location AMC), Department of Medical Biology, Meibergdreef 9, 1005 AZ, Amsterdam, The Netherlands.
  • Putker K; Department of Experimental Cardiology, Amsterdam UMC (Location AMC), Meibergdreef 9, 1005 AZ, Amsterdam, The Netherlands.
  • van Amersfoorth SCM; Department of Human Genetics, Leiden University Medical Center, Albinusdreef 2, 2333 ZA, Leiden, The Netherlands.
  • Aartsma-Rus A; Department of Experimental Cardiology, Amsterdam UMC (Location AMC), Meibergdreef 9, 1005 AZ, Amsterdam, The Netherlands.
  • Lodder EM; Department of Human Genetics, Leiden University Medical Center, Albinusdreef 2, 2333 ZA, Leiden, The Netherlands.
  • Remme CA; Department of Experimental Cardiology, Amsterdam UMC (Location AMC), Meibergdreef 9, 1005 AZ, Amsterdam, The Netherlands.
Sci Rep ; 11(1): 9779, 2021 05 07.
Article en En | MEDLINE | ID: mdl-33963238

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Distrofina / Distrofia Muscular de Duchenne / Miocitos Cardíacos / Electrofisiología Cardíaca / Miocardio Tipo de estudio: Prognostic_studies Límite: Animals Idioma: En Revista: Sci Rep Año: 2021 Tipo del documento: Article País de afiliación: Países Bajos Pais de publicación: Reino Unido

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Distrofina / Distrofia Muscular de Duchenne / Miocitos Cardíacos / Electrofisiología Cardíaca / Miocardio Tipo de estudio: Prognostic_studies Límite: Animals Idioma: En Revista: Sci Rep Año: 2021 Tipo del documento: Article País de afiliación: Países Bajos Pais de publicación: Reino Unido