[Coexistence of IgG4-related autoimmune hepatitis and inflammatory pseudotumors of the liver:a case report].
Nihon Shokakibyo Gakkai Zasshi
; 117(6): 532-541, 2020.
Article
en Ja
| MEDLINE
| ID: mdl-32565511
IgG4-related autoimmune hepatitis (IgG4-AIH) is characterized by hepatic inflammation and is considered an IgG4-related disease. Several inflammatory pseudotumors (IPTs) are also considered as IgG4-related diseases;however, there have been no reports of cases wherein both diseases occurred concurrently. An older adult with liver dysfunction was admitted to the hospital and was diagnosed with IgG4-AIH following a liver biopsy;IgG4-positive plasma cell infiltration in the portal tract and high serum IgG4 concentration were detected. A few months following biopsy, imaging studies revealed two IPTs in the liver. The patient was diagnosed with cryptogenic organized pneumonia several months after imaging and was treated with steroids in a different hospital. Her liver dysfunction improved, and one of the two IPTs disappeared in response to steroid treatment. The following is an account of a rare case of IgG4-AIH with IPTs of the liver.
Texto completo:
1
Colección:
01-internacional
Base de datos:
MEDLINE
Asunto principal:
Enfermedades Autoinmunes
/
Hepatitis Autoinmune
/
Granuloma de Células Plasmáticas
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Hepatopatías
Límite:
Aged
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Female
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Humans
Idioma:
Ja
Revista:
Nihon Shokakibyo Gakkai Zasshi
Año:
2020
Tipo del documento:
Article
Pais de publicación:
Japón