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Klippel-Trenaunay-Weber Syndrome Associated with Multiple Cerebral Arteriovenous Malformations: Usefulness of Gamma Knife Stereotactic Radiosurgery in This Syndrome.
Pérez-Alfayate, Rebeca; Martínez-Moreno, Nuria; Rosati, Santiago Dario; Moreu-Gamazo, Manuel; Pérez-García, Carlos; Martínez-Alvarez, Roberto.
Afiliación
  • Pérez-Alfayate R; Neurosurgery Department, Neuroscience Institute, Hospital Clínico San Carlos, Madrid, Spain. Electronic address: rebecap.alfayate@gmail.com.
  • Martínez-Moreno N; Gamma-Knife Radiosurgery Unit, Hospital Ruber Internacional, Madrid, Spain.
  • Rosati SD; Interventional Neuroradiology Unit, Radiology Department, Hospital Clínico San Carlos, Madrid, Spain.
  • Moreu-Gamazo M; Interventional Neuroradiology Unit, Radiology Department, Hospital Clínico San Carlos, Madrid, Spain.
  • Pérez-García C; Interventional Neuroradiology Unit, Radiology Department, Hospital Clínico San Carlos, Madrid, Spain.
  • Martínez-Alvarez R; Gamma-Knife Radiosurgery Unit, Hospital Ruber Internacional, Madrid, Spain.
World Neurosurg ; 141: 425-429, 2020 09.
Article en En | MEDLINE | ID: mdl-32534263
BACKGROUND: Klippel-Trenaunay-Weber syndrome (KTWS) is characterized by the presence of a combined vascular malformation of capillaries, veins, and lymphatic vessels; congenital venous abnormalities; and limb hypertrophy. Its association with neurovascular abnormalities is infrequent, and the presence of intracranial arteriovenous malformations (AVMs) is extremely rare. CASE DESCRIPTION: We report a case of a 48-year-old male diagnosed with KTWS who spontaneously presented with a cerebral hemorrhage. Computed tomography scan and angio-computed tomography studies revealed bleeding associated with AVM rupture. In the conventional arteriography study, 10 small (<1 cm) AVMs were observed. The patient presented a good clinical recovery. These multiple small lesions were not considered susceptible to surgical or endovascular treatments. Therefore all lesions were treated with Gamma Knife stereotactic radiosurgery since it attains the highest dose drop and minimal irradiation of the healthy parenchyma. One year after the treatment, the lesions have shrunk. CONCLUSIONS: Cerebral AVMs are extremely rare in KTWS cases; however, their presence can have serious consequences if they are treated. We find it advisable to include brain imaging tests, such as nuclear magnetic resonance imaging, to diagnose and monitor KTWS. Furthermore, a Gamma Knife may be useful when multiple AVMs are present.
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Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Malformaciones Arteriovenosas Intracraneales / Hemorragia Cerebral / Síndrome de Klippel-Trenaunay-Weber Tipo de estudio: Diagnostic_studies / Risk_factors_studies Límite: Humans / Male / Middle aged Idioma: En Revista: World Neurosurg Asunto de la revista: NEUROCIRURGIA Año: 2020 Tipo del documento: Article Pais de publicación: Estados Unidos
Texto completo
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Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Malformaciones Arteriovenosas Intracraneales / Hemorragia Cerebral / Síndrome de Klippel-Trenaunay-Weber Tipo de estudio: Diagnostic_studies / Risk_factors_studies Límite: Humans / Male / Middle aged Idioma: En Revista: World Neurosurg Asunto de la revista: NEUROCIRURGIA Año: 2020 Tipo del documento: Article Pais de publicación: Estados Unidos