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Chimeric Peptide Species Contribute to Divergent Dipeptide Repeat Pathology in c9ALS/FTD and SCA36.
McEachin, Zachary T; Gendron, Tania F; Raj, Nisha; García-Murias, María; Banerjee, Anwesha; Purcell, Ryan H; Ward, Patricia J; Todd, Tiffany W; Merritt-Garza, Megan E; Jansen-West, Karen; Hales, Chadwick M; García-Sobrino, Tania; Quintáns, Beatriz; Holler, Christopher J; Taylor, Georgia; San Millán, Beatriz; Teijeira, Susana; Yamashita, Toru; Ohkubo, Ryuichi; Boulis, Nicholas M; Xu, Chongchong; Wen, Zhexing; Streichenberger, Nathalie; Fogel, Brent L; Kukar, Thomas; Abe, Koji; Dickson, Dennis W; Arias, Manuel; Glass, Jonathan D; Jiang, Jie; Tansey, Malú G; Sobrido, María-Jesús; Petrucelli, Leonard; Rossoll, Wilfried; Bassell, Gary J.
Afiliación
  • McEachin ZT; Department of Cell Biology, Emory University, Atlanta, GA 30322, USA; Laboratory for Translational Cell Biology, Emory University, Atlanta, GA 30322, USA; Wallace H. Coulter Graduate Program in Biomedical Engineering, Georgia Institute of Technology & Emory University, Atlanta, GA 30332, USA. El
  • Gendron TF; Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA; Mayo Clinic Graduate School of Biomedical Sciences, Mayo Clinic, Jacksonville, FL 32224, USA.
  • Raj N; Department of Cell Biology, Emory University, Atlanta, GA 30322, USA; Laboratory for Translational Cell Biology, Emory University, Atlanta, GA 30322, USA.
  • García-Murias M; Centro de Investigación Biomédica en red de Enfermedades Raras (CIBERER), Santiago de Compostela, Spain; Neurogenetics Research Group, Instituto de Investigación Sanitaria (IDIS), Hospital Clínico Universitario, SERGAS, Santiago de Compostela, Spain.
  • Banerjee A; Department of Cell Biology, Emory University, Atlanta, GA 30322, USA.
  • Purcell RH; Department of Cell Biology, Emory University, Atlanta, GA 30322, USA; Laboratory for Translational Cell Biology, Emory University, Atlanta, GA 30322, USA.
  • Ward PJ; Department of Cell Biology, Emory University, Atlanta, GA 30322, USA.
  • Todd TW; Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA.
  • Merritt-Garza ME; Laboratory for Translational Cell Biology, Emory University, Atlanta, GA 30322, USA.
  • Jansen-West K; Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA.
  • Hales CM; Department of Neurology, Emory University, Atlanta, GA 30322, USA.
  • García-Sobrino T; Department of Neurology, Hospital Clínico Universitario, SERGAS, Santiago de Compostela, Spain.
  • Quintáns B; Centro de Investigación Biomédica en red de Enfermedades Raras (CIBERER), Santiago de Compostela, Spain; Neurogenetics Research Group, Instituto de Investigación Sanitaria (IDIS), Hospital Clínico Universitario, SERGAS, Santiago de Compostela, Spain.
  • Holler CJ; Department of Pharmacology & Chemical Biology, Emory University, Atlanta, GA 30322, USA.
  • Taylor G; Department of Pharmacology & Chemical Biology, Emory University, Atlanta, GA 30322, USA.
  • San Millán B; Rare Diseases and Pediatric Medicine Research Group, Galicia Sur Health Research Institute (IIS Galicia Sur), SERGAS-UVIGO, Vigo, Spain; Pathology Department, Complexo Hospitalario Universitario de Vigo (CHUVI), SERGAS, Vigo, Spain.
  • Teijeira S; Rare Diseases and Pediatric Medicine Research Group, Galicia Sur Health Research Institute (IIS Galicia Sur), SERGAS-UVIGO, Vigo, Spain; Pathology Department, Complexo Hospitalario Universitario de Vigo (CHUVI), SERGAS, Vigo, Spain.
  • Yamashita T; Department of Neurology, Okayama University, Okayama, Japan.
  • Ohkubo R; Department of Neurology, Fujimoto General Hospital, Miyazaki, Japan.
  • Boulis NM; Department of Neurosurgery, Emory University, Atlanta, GA 30322, USA.
  • Xu C; Department of Psychiatry & Behavioral Sciences, Emory University, Atlanta, GA 30322, USA.
  • Wen Z; Department of Cell Biology, Emory University, Atlanta, GA 30322, USA; Laboratory for Translational Cell Biology, Emory University, Atlanta, GA 30322, USA; Department of Neurology, Emory University, Atlanta, GA 30322, USA; Department of Psychiatry & Behavioral Sciences, Emory University, Atlanta,
  • Streichenberger N; Hospices Civils de Lyon, Lyon, France; Université Claude Bernard Lyon, Lyon, France; Institut NeuroMyogène CNRS UMR 5310.
  • Fogel BL; Department of Neurology & Human Genetics, David Geffen School of Medicine, University of California Los Angeles, Los Angeles, CA 90095, USA.
  • Kukar T; Department of Neurology, Emory University, Atlanta, GA 30322, USA; Department of Pharmacology & Chemical Biology, Emory University, Atlanta, GA 30322, USA.
  • Abe K; Department of Neurology, Okayama University, Okayama, Japan.
  • Dickson DW; Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA.
  • Arias M; Neurogenetics Research Group, Instituto de Investigación Sanitaria (IDIS), Hospital Clínico Universitario, SERGAS, Santiago de Compostela, Spain; Department of Neurology, Hospital Clínico Universitario, SERGAS, Santiago de Compostela, Spain.
  • Glass JD; Department of Neurology, Emory University, Atlanta, GA 30322, USA.
  • Jiang J; Department of Cell Biology, Emory University, Atlanta, GA 30322, USA.
  • Tansey MG; Department of Neuroscience, University of Florida, Gainesville, FL 32607, USA; Center for Translational Research in Neurodegenerative Disease, University of Florida, Gainesville, FL 32607, USA; Norman Fixel Institute for Neurological Diseases, University of Florida, Gainesville, FL 32607, USA.
  • Sobrido MJ; Centro de Investigación Biomédica en red de Enfermedades Raras (CIBERER), Santiago de Compostela, Spain; Neurogenetics Research Group, Instituto de Investigación Sanitaria (IDIS), Hospital Clínico Universitario, SERGAS, Santiago de Compostela, Spain.
  • Petrucelli L; Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA; Mayo Clinic Graduate School of Biomedical Sciences, Mayo Clinic, Jacksonville, FL 32224, USA.
  • Rossoll W; Department of Neuroscience, Mayo Clinic, Jacksonville, FL 32224, USA; Mayo Clinic Graduate School of Biomedical Sciences, Mayo Clinic, Jacksonville, FL 32224, USA.
  • Bassell GJ; Department of Cell Biology, Emory University, Atlanta, GA 30322, USA; Laboratory for Translational Cell Biology, Emory University, Atlanta, GA 30322, USA; Wallace H. Coulter Graduate Program in Biomedical Engineering, Georgia Institute of Technology & Emory University, Atlanta, GA 30332, USA; De
Neuron ; 107(2): 292-305.e6, 2020 07 22.
Article en En | MEDLINE | ID: mdl-32375063

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Ataxias Espinocerebelosas / Dipéptidos / Proteínas Mutantes Quiméricas / Demencia Frontotemporal / Proteína C9orf72 / Esclerosis Amiotrófica Lateral Límite: Animals / Female / Humans / Pregnancy Idioma: En Revista: Neuron Asunto de la revista: NEUROLOGIA Año: 2020 Tipo del documento: Article Pais de publicación: Estados Unidos

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Ataxias Espinocerebelosas / Dipéptidos / Proteínas Mutantes Quiméricas / Demencia Frontotemporal / Proteína C9orf72 / Esclerosis Amiotrófica Lateral Límite: Animals / Female / Humans / Pregnancy Idioma: En Revista: Neuron Asunto de la revista: NEUROLOGIA Año: 2020 Tipo del documento: Article Pais de publicación: Estados Unidos