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Nutritional ketosis improves exercise metabolism in patients with very long-chain acyl-CoA dehydrogenase deficiency.
Bleeker, Jeannette C; Visser, Gepke; Clarke, Kieran; Ferdinandusse, Sacha; de Haan, Ferdinand H; Houtkooper, Riekelt H; IJlst, Lodewijk; Kok, Irene L; Langeveld, Mirjam; van der Pol, W Ludo; de Sain-van der Velden, Monique G M; Sibeijn-Kuiper, Anita; Takken, Tim; Wanders, Ronald J A; van Weeghel, Michel; Wijburg, Frits A; van der Woude, Luc H; Wüst, Rob C I; Cox, Pete J; Jeneson, Jeroen A L.
Afiliación
  • Bleeker JC; Department of Metabolic Diseases, Wilhelmina Children's Hospital, University Medical Center Utrecht, Utrecht, The Netherlands.
  • Visser G; Department of Metabolic Diseases, Emma Children's Hospital, Amsterdam UMC, University of Amsterdam, Amsterdam, The Netherlands.
  • Clarke K; Department of Metabolic Diseases, Wilhelmina Children's Hospital, University Medical Center Utrecht, Utrecht, The Netherlands.
  • Ferdinandusse S; Department of Metabolic Diseases, Emma Children's Hospital, Amsterdam UMC, University of Amsterdam, Amsterdam, The Netherlands.
  • de Haan FH; Department of Physiology, Anatomy and Genetics, University of Oxford, Oxford, UK.
  • Houtkooper RH; Laboratory Genetic Metabolic Diseases, Amsterdam Gastroenterology and Metabolism, Amsterdam UMC, University of Amsterdam, Amsterdam, The Netherlands.
  • IJlst L; ACHIEVE, Center for Applied Research, Faculty of Health, University of Applied Sciences Amsterdam, Amsterdam, The Netherlands.
  • Kok IL; Laboratory Genetic Metabolic Diseases, Amsterdam Gastroenterology and Metabolism, Amsterdam UMC, University of Amsterdam, Amsterdam, The Netherlands.
  • Langeveld M; Laboratory Genetic Metabolic Diseases, Amsterdam Gastroenterology and Metabolism, Amsterdam UMC, University of Amsterdam, Amsterdam, The Netherlands.
  • van der Pol WL; Department of Metabolic Diseases, Wilhelmina Children's Hospital, University Medical Center Utrecht, Utrecht, The Netherlands.
  • de Sain-van der Velden MGM; Department of Endocrinology and Metabolism, Amsterdam UMC, University of Amsterdam, Amsterdam, The Netherlands.
  • Sibeijn-Kuiper A; Department of Neurology and Neurosurgery, Rudolf Magnus Institute of Neuroscience, Spieren voor Spieren Kindercentrum, University Medical Center Utrecht, Utrecht, The Netherlands.
  • Takken T; Department of Metabolic Diseases, Wilhelmina Children's Hospital, University Medical Center Utrecht, Utrecht, The Netherlands.
  • Wanders RJA; Neuroimaging Center, Department of Biomedical Sciences of Cells and Systems, University Medical Center Groningen, Groningen, The Netherlands.
  • van Weeghel M; Center for Child Development & Exercise, Department of Medical Physiology, University Medical Center Utrecht, Utrecht, The Netherlands.
  • Wijburg FA; Department of Metabolic Diseases, Emma Children's Hospital, Amsterdam UMC, University of Amsterdam, Amsterdam, The Netherlands.
  • van der Woude LH; Laboratory Genetic Metabolic Diseases, Amsterdam Gastroenterology and Metabolism, Amsterdam UMC, University of Amsterdam, Amsterdam, The Netherlands.
  • Wüst RCI; Laboratory Genetic Metabolic Diseases, Amsterdam Gastroenterology and Metabolism, Amsterdam UMC, University of Amsterdam, Amsterdam, The Netherlands.
  • Cox PJ; Laboratory Genetic Metabolic Diseases, Amsterdam UMC, University of Amsterdam, Amsterdam Cardiovascular Sciences, Amsterdam, The Netherlands.
  • Jeneson JAL; Core Facility Metabolomics, Amsterdam UMC, University of Amsterdam, Amsterdam, The Netherlands.
J Inherit Metab Dis ; 43(4): 787-799, 2020 07.
Article en En | MEDLINE | ID: mdl-31955429

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Bebidas / Enfermedades Mitocondriales / Entrenamiento Aeróbico / Síndromes Congénitos de Insuficiencia de la Médula Ósea / Cetosis / Errores Innatos del Metabolismo Lipídico / Enfermedades Musculares Tipo de estudio: Clinical_trials / Guideline Límite: Adolescent / Adult / Female / Humans / Male / Middle aged País/Región como asunto: Europa Idioma: En Revista: J Inherit Metab Dis Año: 2020 Tipo del documento: Article País de afiliación: Países Bajos Pais de publicación: Estados Unidos

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Bebidas / Enfermedades Mitocondriales / Entrenamiento Aeróbico / Síndromes Congénitos de Insuficiencia de la Médula Ósea / Cetosis / Errores Innatos del Metabolismo Lipídico / Enfermedades Musculares Tipo de estudio: Clinical_trials / Guideline Límite: Adolescent / Adult / Female / Humans / Male / Middle aged País/Región como asunto: Europa Idioma: En Revista: J Inherit Metab Dis Año: 2020 Tipo del documento: Article País de afiliación: Países Bajos Pais de publicación: Estados Unidos