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A homozygous SFTPA1 mutation drives necroptosis of type II alveolar epithelial cells in patients with idiopathic pulmonary fibrosis.
Takezaki, Akio; Tsukumo, Shin-Ichi; Setoguchi, Yasuhiro; Ledford, Julie G; Goto, Hisatsugu; Hosomichi, Kazuyoshi; Uehara, Hisanori; Nishioka, Yasuhiko; Yasutomo, Koji.
Afiliación
  • Takezaki A; Department of Immunology & Parasitology, Graduate School of Medicine, Tokushima University, Tokushima, Japan.
  • Tsukumo SI; Department of Respiratory Medicine, Graduate School of Medicine, Tokushima University, Tokushima, Japan.
  • Setoguchi Y; Department of Immunology & Parasitology, Graduate School of Medicine, Tokushima University, Tokushima, Japan.
  • Ledford JG; Department of Interdisciplinary Researches for Medicine and Photonics, Institute of Post-LED Photonics, Tokushima University, Tokushima, Japan.
  • Goto H; Department of Respiratory Medicine, Graduate School of Medicine, Tokyo Medical University, Tokyo, Japan.
  • Hosomichi K; Department of Respiratory Medicine, Graduate School of Medical and Dental Sciences, Tokyo Medical and Dental University, Tokyo, Japan.
  • Uehara H; Department of Cellular and Molecular Medicine, University of Arizona, Tucson, AZ.
  • Nishioka Y; Department of Respiratory Medicine, Graduate School of Medicine, Tokushima University, Tokushima, Japan.
  • Yasutomo K; Department of Bioinformatics and Genomics, Graduate School of Advanced Preventive Medical Sciences, Kanazawa University, Ishikawa, Japan.
J Exp Med ; 216(12): 2724-2735, 2019 12 02.
Article en En | MEDLINE | ID: mdl-31601679

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Proteína A Asociada a Surfactante Pulmonar / Fibrosis Pulmonar Idiopática / Células Epiteliales Alveolares / Homocigoto / Mutación Tipo de estudio: Prognostic_studies Límite: Adult / Animals / Female / Humans / Male Idioma: En Revista: J Exp Med Año: 2019 Tipo del documento: Article País de afiliación: Japón Pais de publicación: Estados Unidos

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Proteína A Asociada a Surfactante Pulmonar / Fibrosis Pulmonar Idiopática / Células Epiteliales Alveolares / Homocigoto / Mutación Tipo de estudio: Prognostic_studies Límite: Adult / Animals / Female / Humans / Male Idioma: En Revista: J Exp Med Año: 2019 Tipo del documento: Article País de afiliación: Japón Pais de publicación: Estados Unidos