Your browser doesn't support javascript.
loading
Bilateral Superior Semicircular Canal Dehiscence Associated with Ehlers-Danlos Syndrome: A Report of 2 Cases.
Preet, Komal; Udawatta, Methma; Duong, Courtney; Gopen, Quinton; Yang, Isaac.
Afiliación
  • Preet K; Department of Neurosurgery, Ronald Reagan UCLA Medical Center, Los Angeles, California, USA.
  • Udawatta M; Department of Neurosurgery, Ronald Reagan UCLA Medical Center, Los Angeles, California, USA.
  • Duong C; Department of Neurosurgery, Ronald Reagan UCLA Medical Center, Los Angeles, California, USA.
  • Gopen Q; Department of Head and Neck Surgery, Ronald Reagan UCLA Medical Center, Los Angeles, California, USA.
  • Yang I; Department of Neurosurgery, Ronald Reagan UCLA Medical Center, Los Angeles, California, USA; Department of Head and Neck Surgery, Ronald Reagan UCLA Medical Center, Los Angeles, California, USA; Department of Radiation Oncology, Ronald Reagan UCLA Medical Center, Los Angeles, California, USA; Office
World Neurosurg ; 122: 161-164, 2019 Feb.
Article en En | MEDLINE | ID: mdl-30385359
BACKGROUND: Superior semicircular canal dehiscence (SSCD) is a rare bony defect in the petrosal temporal bone, creating a new opening between the inner ear and middle cranial fossa. Ehlers-Danlos syndrome (EDS) is an inherited connective tissue disorder characterized by a defect in collagen synthesis. Patients with EDS are more likely to have bony abnormalities, which may predispose them to developing SSCD. CASE DESCRIPTION: We report the cases of 2 women with history of EDS hypermobility type (HT). Both patients presented with bilateral auditory and vestibular symptoms, and computed tomography scan confirmed the presence of bilateral dehiscence in their superior semicircular canals. They underwent elective surgical repair via middle fossa craniotomy and report improvement in their symptoms. CONCLUSIONS: Because of the rarity of both diseases and their pathophysiology, a history of EDS may predispose an individual to developing SSCD. Although further research is necessary, this report aims to improve clinical screening of patients with EDS HT by suggesting an auditory and vestibular evaluation and assessment of pertinent bony abnormalities.
Asunto(s)
Palabras clave
Texto completo
Añadir a Mi BVS
Imprimir
XML
PubMed Links
Buscar en Google

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Hueso Temporal / Síndrome de Ehlers-Danlos / Enfermedades del Laberinto Tipo de estudio: Diagnostic_studies / Risk_factors_studies Límite: Adult / Female / Humans / Middle aged Idioma: En Revista: World Neurosurg Asunto de la revista: NEUROCIRURGIA Año: 2019 Tipo del documento: Article País de afiliación: Estados Unidos Pais de publicación: Estados Unidos
Texto completo
Añadir a Mi BVS
Imprimir
XML
PubMed Links
Buscar en Google

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Hueso Temporal / Síndrome de Ehlers-Danlos / Enfermedades del Laberinto Tipo de estudio: Diagnostic_studies / Risk_factors_studies Límite: Adult / Female / Humans / Middle aged Idioma: En Revista: World Neurosurg Asunto de la revista: NEUROCIRURGIA Año: 2019 Tipo del documento: Article País de afiliación: Estados Unidos Pais de publicación: Estados Unidos