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Effect of diazoxide on Friedreich ataxia models.
Santoro, Antonella; Anjomani Virmouni, Sara; Paradies, Eleonora; Villalobos Coa, Valentina L; Al-Mahdawi, Sahar; Khoo, Mee; Porcelli, Vito; Vozza, Angelo; Perrone, Mara; Denora, Nunzio; Taroni, Franco; Merla, Giuseppe; Palmieri, Luigi; Pook, Mark A; Marobbio, Carlo M T.
Afiliación
  • Santoro A; Institute of Biomembranes, Bioenergetics and Molecular Biotechnologies, Consiglio Nazionale delle Ricerche, 70126 Bari, Italy.
  • Anjomani Virmouni S; Department of Life Sciences, College of Health & Life Sciences, Brunel University London, Uxbridge UB8 3PH, UK.
  • Paradies E; Institute of Biomembranes, Bioenergetics and Molecular Biotechnologies, Consiglio Nazionale delle Ricerche, 70126 Bari, Italy.
  • Villalobos Coa VL; Department of Biosciences, Biotechnologies and Biopharmaceutics, University of Bari, 70125 Bari, Italy.
  • Al-Mahdawi S; Department of Life Sciences, College of Health & Life Sciences, Brunel University London, Uxbridge UB8 3PH, UK.
  • Khoo M; Department of Life Sciences, College of Health & Life Sciences, Brunel University London, Uxbridge UB8 3PH, UK.
  • Porcelli V; Department of Biosciences, Biotechnologies and Biopharmaceutics, University of Bari, 70125 Bari, Italy.
  • Vozza A; Department of Biosciences, Biotechnologies and Biopharmaceutics, University of Bari, 70125 Bari, Italy.
  • Perrone M; Department of Pharmacy - Drug Sciences, University of Bari, 70125 Bari, Italy.
  • Denora N; Department of Pharmacy - Drug Sciences, University of Bari, 70125 Bari, Italy.
  • Taroni F; Unit of Genetics of Neurodegenerative and Metabolic Diseases, Fondazione IRCCS-Istituto Neurologico Carlo Besta, 20133 Milan, Italy.
  • Merla G; Medical Genetics Unit, IRCCS Casa Sollievo della Sofferenza, 71013 San Giovanni, Rotondo, Italy.
  • Palmieri L; Institute of Biomembranes, Bioenergetics and Molecular Biotechnologies, Consiglio Nazionale delle Ricerche, 70126 Bari, Italy.
  • Pook MA; Department of Biosciences, Biotechnologies and Biopharmaceutics, University of Bari, 70125 Bari, Italy.
  • Marobbio CMT; Department of Life Sciences, College of Health & Life Sciences, Brunel University London, Uxbridge UB8 3PH, UK.
Hum Mol Genet ; 27(6): 992-1001, 2018 03 15.
Article en En | MEDLINE | ID: mdl-29325032

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Ataxia de Friedreich / Proteínas de Unión a Hierro / Diazóxido Tipo de estudio: Prognostic_studies Límite: Animals / Humans Idioma: En Revista: Hum Mol Genet Asunto de la revista: BIOLOGIA MOLECULAR / GENETICA MEDICA Año: 2018 Tipo del documento: Article País de afiliación: Italia Pais de publicación: Reino Unido

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Ataxia de Friedreich / Proteínas de Unión a Hierro / Diazóxido Tipo de estudio: Prognostic_studies Límite: Animals / Humans Idioma: En Revista: Hum Mol Genet Asunto de la revista: BIOLOGIA MOLECULAR / GENETICA MEDICA Año: 2018 Tipo del documento: Article País de afiliación: Italia Pais de publicación: Reino Unido