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Evidence of oxidative stress and mitochondrial dysfunction in spinocerebellar ataxia type 2 (SCA2) patient fibroblasts: Effect of coenzyme Q10 supplementation on these parameters.
Cornelius, Nanna; Wardman, Jonathan H; Hargreaves, Iain P; Neergheen, Viruna; Bie, Anne Sigaard; Tümer, Zeynep; Nielsen, Jørgen E; Nielsen, Troels T.
Afiliación
  • Cornelius N; Neurogenetics Research Laboratory, Danish Dementia Research Centre, Department of Neurology, Rigshospitalet, University of Copenhagen, Denmark.
  • Wardman JH; Neurogenetics Research Laboratory, Danish Dementia Research Centre, Department of Neurology, Rigshospitalet, University of Copenhagen, Denmark.
  • Hargreaves IP; Pharmacy and Biomolecular Sciences, James Parsons Building, John Moore's University, Liverpool L3 3AF, United Kingdom.
  • Neergheen V; Neurometabolic Unit, National Hospital for Neurology and Neurosurgery, Queen Square, London, United Kingdom.
  • Bie AS; Neurogenetics Research Laboratory, Danish Dementia Research Centre, Department of Neurology, Rigshospitalet, University of Copenhagen, Denmark.
  • Tümer Z; Applied Human Molecular Genetics, Kennedy Center, Department of Clinical Genetics, Rigshospitalet, Glostrup, University of Copenhagen, Denmark.
  • Nielsen JE; Neurogenetics Research Laboratory, Danish Dementia Research Centre, Department of Neurology, Rigshospitalet, University of Copenhagen, Denmark; Danish Dementia Research Centre, Neurogenetics Clinic, Department of Neurology, Rigshospitalet, University of Copenhagen, Denmark; Section of Neurogenetics,
  • Nielsen TT; Neurogenetics Research Laboratory, Danish Dementia Research Centre, Department of Neurology, Rigshospitalet, University of Copenhagen, Denmark.
Mitochondrion ; 34: 103-114, 2017 05.
Article en En | MEDLINE | ID: mdl-28263872

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Vitaminas / Ubiquinona / Estrés Oxidativo / Ataxias Espinocerebelosas / Fibroblastos / Mitocondrias Límite: Adolescent / Adult / Aged / Female / Humans / Male / Middle aged Idioma: En Revista: Mitochondrion Año: 2017 Tipo del documento: Article País de afiliación: Dinamarca Pais de publicación: Países Bajos

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Vitaminas / Ubiquinona / Estrés Oxidativo / Ataxias Espinocerebelosas / Fibroblastos / Mitocondrias Límite: Adolescent / Adult / Aged / Female / Humans / Male / Middle aged Idioma: En Revista: Mitochondrion Año: 2017 Tipo del documento: Article País de afiliación: Dinamarca Pais de publicación: Países Bajos