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Overlapping 16p13.11 deletion and gain of copies variations associated with childhood onset psychosis include genes with mechanistic implications for autism associated pathways: Two case reports.
Brownstein, Catherine A; Kleiman, Robin J; Engle, Elizabeth C; Towne, Meghan C; D'Angelo, Eugene J; Yu, Timothy W; Beggs, Alan H; Picker, Jonathan; Fogler, Jason M; Carroll, Devon; Schmitt, Rachel C O; Wolff, Robert R; Shen, Yiping; Lip, Va; Bilguvar, Kaya; Kim, April; Tembulkar, Sahil; O'Donnell, Kyle; Gonzalez-Heydrich, Joseph.
Afiliación
  • Brownstein CA; The Manton Center for Orphan Disease Research, Boston Children's Hospital, Boston, Massachusetts.
  • Kleiman RJ; Division of Genetics and Genomics, Boston Children's Hospital, Boston, Massachusetts.
  • Engle EC; Department of Pediatrics, Harvard Medical School, Boston, Massachusetts.
  • Towne MC; Translational Neuroscience Center, Boston Children's Hospital, Boston, Massachusetts.
  • D'Angelo EJ; FM Kirby Neurobiology Center, Boston Children's Hospital, Boston, Massachusetts.
  • Yu TW; Department of Neurology, Harvard Medical School, Boston, Massachusetts.
  • Beggs AH; Department of Neurology, Boston Children's Hospital, Boston, Massachusetts.
  • Picker J; The Manton Center for Orphan Disease Research, Boston Children's Hospital, Boston, Massachusetts.
  • Fogler JM; Division of Genetics and Genomics, Boston Children's Hospital, Boston, Massachusetts.
  • Carroll D; FM Kirby Neurobiology Center, Boston Children's Hospital, Boston, Massachusetts.
  • Schmitt RC; Department of Neurology, Harvard Medical School, Boston, Massachusetts.
  • Wolff RR; Department of Neurology, Boston Children's Hospital, Boston, Massachusetts.
  • Shen Y; Department of Ophthalmology, Boston Children's Hospital, Boston, Massachusetts.
  • Lip V; Department of Ophthalmology, Harvard Medical School, Boston, Massachusetts.
  • Bilguvar K; Howard Hughes Medical Institute, Chevy Chase, Maryland.
  • Kim A; The Manton Center for Orphan Disease Research, Boston Children's Hospital, Boston, Massachusetts.
  • Tembulkar S; Division of Genetics and Genomics, Boston Children's Hospital, Boston, Massachusetts.
  • O'Donnell K; Division of Psychology, Department of Psychiatry, Boston Children's Hospital, Boston, Massachusetts.
  • Gonzalez-Heydrich J; Department of Psychiatry, Harvard Medical School, Boston, Massachusetts.
Am J Med Genet A ; 170A(5): 1165-73, 2016 May.
Article en En | MEDLINE | ID: mdl-26887912
Copy number variability at 16p13.11 has been associated with intellectual disability, autism, schizophrenia, epilepsy, and attention-deficit hyperactivity disorder. Adolescent/adult- onset psychosis has been reported in a subset of these cases. Here, we report on two children with CNVs in 16p13.11 that developed psychosis before the age of 7. The genotype and neuropsychiatric abnormalities of these patients highlight several overlapping genes that have possible mechanistic relevance to pathways previously implicated in Autism Spectrum Disorders, including the mTOR signaling and the ubiquitin-proteasome cascades. A careful screening of the 16p13.11 region is warranted in patients with childhood onset psychosis.
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Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Trastornos Psicóticos / Esquizofrenia / Trastorno Autístico / Cromosomas Humanos Par 16 / Discapacidades del Desarrollo Tipo de estudio: Prognostic_studies / Risk_factors_studies Límite: Child / Child, preschool / Female / Humans / Male Idioma: En Revista: Am J Med Genet A Asunto de la revista: GENETICA MEDICA Año: 2016 Tipo del documento: Article Pais de publicación: Estados Unidos

Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Trastornos Psicóticos / Esquizofrenia / Trastorno Autístico / Cromosomas Humanos Par 16 / Discapacidades del Desarrollo Tipo de estudio: Prognostic_studies / Risk_factors_studies Límite: Child / Child, preschool / Female / Humans / Male Idioma: En Revista: Am J Med Genet A Asunto de la revista: GENETICA MEDICA Año: 2016 Tipo del documento: Article Pais de publicación: Estados Unidos