Beneath the Copper-Pediatric Wilson's Disease Cirrhosis and Hepatocellular Carcinoma: A Case Report with Literature Review.
Semin Liver Dis
; 35(4): 434-8, 2015 Nov.
Article
en En
| MEDLINE
| ID: mdl-26676818
Primary hepatic malignancies are uncommon in pediatrics. Tumors such as hepatocellular carcinoma (HCC) develop typically in the setting of chronic liver disease. The incidence of HCC in Wilson's disease-related cirrhosis is disproportionately lower than in many other forms of end-stage liver disease. A preadolescent girl presented with Wilson's disease cirrhosis and a HCC requiring orthotopic liver transplantation. This case highlights the need to consider hepatic malignancies even in young Wilson's disease patients. Pediatric Wilson's disease and the hepatic tumor literature are reviewed.
Texto completo:
1
Colección:
01-internacional
Base de datos:
MEDLINE
Asunto principal:
Ceruloplasmina
/
Carcinoma Hepatocelular
/
Degeneración Hepatolenticular
/
Hígado
/
Cirrosis Hepática
/
Neoplasias Hepáticas
Tipo de estudio:
Diagnostic_studies
/
Etiology_studies
Límite:
Child
/
Female
/
Humans
Idioma:
En
Revista:
Semin Liver Dis
Año:
2015
Tipo del documento:
Article
Pais de publicación:
Estados Unidos