Granulomatosis with polyangiitis and constrictive pericarditis--a case report.

Horne, A E; Henriksen, P A; Amft, E N

Horne, A E; Henriksen, P A; Amft, E N.

Afiliación

Horne AE; AE Horne, Rheumatic Diseases Unit, Western General Hospital, Crewe Road, Edinburgh EH4 2XU, UK. Email annamariehorne@nhs.net.

J R Coll Physicians Edinb ; 44(4): 283-5, 2014.

Article en En | MEDLINE | ID: mdl-25516896

RESUMEN

Polyangiitis with granulomatosis, previously known as Wegener's granulomatosis, is a systemic necrotising granulomatous vasculitis. It predominantly affects the upper and lower respiratory tracts and the kidneys, but can potentially affect any organ system. It is diagnosed by clinical features, immunology (anti-neutrophil cytoplasmic antibodies) and histology. Cardiac involvement occurs in 6 to 44% of cases. We present a case of polyangiitis with granulomatosis and constrictive pericarditis, which occurred despite vigorous immunosuppression and which required surgical pericardectomy.

Asunto(s)

Granulomatosis con Poliangitis/complicaciones; Pericarditis Constrictiva/etiología; Adulto; Colchicina/uso terapéutico; Disnea/etiología; Ecocardiografía Doppler; Femenino; Humanos; Pericarditis Constrictiva/diagnóstico; Pericarditis Constrictiva/tratamiento farmacológico

Palabras clave

GPA; Wegener's granulomatosis; breathless; pericardial constriction; pericardial stripping

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Texto completo: 1 Colección: 01-internacional Base de datos: MEDLINE Asunto principal: Pericarditis Constrictiva / Granulomatosis con Poliangitis Tipo de estudio: Diagnostic_studies / Etiology_studies Límite: Adult / Female / Humans Idioma: En Revista: J R Coll Physicians Edinb Asunto de la revista: EDUCACAO / HISTORIA DA MEDICINA / MEDICINA Año: 2014 Tipo del documento: Article Pais de publicación: Reino Unido

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