Presenting manifestations of hemophagocytic syndrome in a male patient with systemic lupus erythematosus.
Rheumatol Int
; 30(3): 387-8, 2010 Jan.
Article
en En
| MEDLINE
| ID: mdl-19381636
Hemophagocytic syndrome (HPS) is an unusual but sometimes fatal disorder. We reported a case of 21-year-old man who developed HPS and SLE simultaneously. Febrile pancytopenia, hyperferritinemia, and abnormal liver function tests were observed. Hemophagocytic cells were observed by means of bone marrow biopsy and diagnosed as HPS. The patient was treated with high-dose prednisolone, resulting in an excellent outcome. Early diagnosis of HPS by bone marrow biopsy is important for the successful treatment.
Texto completo:
1
Colección:
01-internacional
Base de datos:
MEDLINE
Asunto principal:
Linfohistiocitosis Hemofagocítica
/
Lupus Eritematoso Sistémico
Tipo de estudio:
Etiology_studies
/
Screening_studies
Límite:
Adult
/
Humans
/
Male
País/Región como asunto:
Asia
Idioma:
En
Revista:
Rheumatol Int
Año:
2010
Tipo del documento:
Article
País de afiliación:
Japón
Pais de publicación:
Alemania