Pentalogy of Cantrell with a double-outlet right ventricle: 3.5-year follow-up in a prenatally diagnosed patient.
Eur J Pediatr
; 167(1): 103-5, 2008 Jan.
Article
en En
| MEDLINE
| ID: mdl-17676339
Pentalogy of Cantrell is a rare congenital defect associated with five ventral midline anomalies and high mortality. An obstetric sonogram revealed a fetus with a body wall defect suggesting a diagnosis of this condition. Soon after birth, the infant underwent a closure of the upper abdominal wall defect followed by the successful repair of double-outlet right ventricle and pulmonary valve stenosis at the age of 5 months. The patient is currently alive and well 3.5 years after surgery. It is concluded that a deliberate therapeutic strategy based on the intrauterine diagnosis may alter the natural history of this devastating disorder.
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Colección:
01-internacional
Base de datos:
MEDLINE
Asunto principal:
Ultrasonografía Prenatal
/
Pared Abdominal
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Pérdida Auditiva
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Cardiopatías Congénitas
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Hernia Umbilical
Tipo de estudio:
Diagnostic_studies
/
Observational_studies
/
Prognostic_studies
/
Risk_factors_studies
Límite:
Adult
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Child, preschool
/
Female
/
Humans
/
Male
/
Newborn
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Pregnancy
Idioma:
En
Revista:
Eur J Pediatr
Año:
2008
Tipo del documento:
Article
País de afiliación:
Japón
Pais de publicación:
Alemania