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Clear cell myomelanocytic tumor of ligamentum teres
Zaidi, Ariba; Chatterjee, Debajyoti; Bhargav, Venu; Gupta, Vikas; Das, Ashim.
Afiliación
  • Zaidi, Ariba; Dr Ram Manohar Lohia Institute of Medical Sciences. Department of Pathology, Lucknow. Uttar Pradesh. IN
  • Chatterjee, Debajyoti; Post Graduate Institute of Medical Education and Research. Department of Histopathology. Chandigarh. IN
  • Bhargav, Venu; Post Graduate Institute of Medical Education and Research. Department of General Surgery. Chandigarh. IN
  • Gupta, Vikas; Post Graduate Institute of Medical Education and Research. Department of General Surgery. Chandigarh. IN
  • Das, Ashim; Post Graduate Institute of Medical Education and Research. Department of Histopathology. Chandigarh. IN
Autops. Case Rep ; 14: e2024503, 2024. tab, graf
Article en En | LILACS-Express | LILACS | ID: biblio-1564011
Biblioteca responsable: BR1.1
Ubicación: 2236-1960-acrep-14-e2024503.xml
ABSTRACT
ABSTRACT Clear cell myomelanocytic tumor (CCMMT) of the falciform ligament/ligamentum teres is a rare hepatic tumor, a variant of the perivascular epithelioid cell tumor (PEComa) family. CCMMT is the rarest variant of hepatic PEComas. Only a few cases of CCMMT have been reported in the English literature. Because of its rarity, less is known about its biological behavior. We present a case of a 31-year-old female who complained of abdominal pain, bilious vomiting, and abdominal fullness over two months. The radiological impression was of focal nodular hyperplasia. The histological examination of the resection specimen revealed a well-circumscribed tumor arranged in fascicles, sheets, and a whorling pattern. The tumor cells were spindle to epithelioid shaped with abundant clear to pale eosinophilic cytoplasm. The tumor cells expressed both myoid (smooth muscle actin) and melanocytic (MelanA and HMB45) markers, while they were negative for hepatocytic and vascular markers. Thus, based on histology and immunohistochemistry, a diagnosis of CCMMT was made. This case presents the diagnostic challenges of CCMMT and discusses the differential diagnosis with a literature review.
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Texto completo: 1 Colección: 01-internacional Base de datos: LILACS Idioma: En Revista: Autops. Case Rep Asunto de la revista: Anatomia / Patologia Cl¡nica / Patologia Legal Año: 2024 Tipo del documento: Article País de afiliación: India Pais de publicación: Brasil

Texto completo: 1 Colección: 01-internacional Base de datos: LILACS Idioma: En Revista: Autops. Case Rep Asunto de la revista: Anatomia / Patologia Cl¡nica / Patologia Legal Año: 2024 Tipo del documento: Article País de afiliación: India Pais de publicación: Brasil