RESUMO
PURPOSE: To analyze speech perception in children with pre-lingual hearing loss with auditory neuropathy spectrum disorder users of bilateral hearing aid. METHODS: This is a descriptive and exploratory study carried out at the Research Center Audiological (HRAC/USP). The study included four children aged between 8 years and 3 months and 12 years and 2 months. Lists of monosyllabic words, two syllables, nonsense words and sentences, the Infant Toddler-Meaningful Auditory Integration Scale (IT-MAIS) and the Meaningful Use of Speech Scale (MUSS), hearing, and language categories were used. All lists were applied in acoustic booth, with speakers, in free field, in silence. RESULTS: The results showed an average 69.5% for the list of monosyllabic words, 87.75% for the list of two-syllable words, 89.92% for the list of nonsense syllables, and 92.5% for the list of sentences. CONCLUSION: The therapeutic process that includes the use of bilateral hearing aid was extremely satisfactory, since it allowed the maximum development of auditory skills.
Assuntos
Auxiliares de Audição , Perda Auditiva Central/reabilitação , Percepção da Fala , Percepção Auditiva , Criança , Implante Coclear , Perda Auditiva Central/cirurgia , Humanos , Desenvolvimento da Linguagem , Masculino , Inquéritos e QuestionáriosRESUMO
RESUMO Objetivo: Analisar a percepção de fala em crianças portadoras de deficiência auditiva pré-lingual com desordem do espectro da neuropatia auditiva (DENA) usuárias de aparelho de amplificação sonora individual (AASI) bilateral. Métodos: Trata-se de um estudo descritivo e exploratório realizado no Centro de Pesquisas Audiológicas da Sessão de Implante Coclear do Hospital de Reabilitação de Anomalias Craniofaciais (HRAC/USP). Foram avaliadas 4 crianças com idade variando entre 8 anos e 3 meses e 12 anos e 2 meses. Foram utilizados: listas de palavras monossílabas, dissílabas, palavras sem sentido e sentenças, Escala de Integração Auditiva Significativa para Crianças Pequenas (IT-MAIS) e Questionário de Avaliação da Linguagem Oral (MUSS), categorias de linguagem e audição. Todas as listas foram aplicadas em cabine acústica, à viva-voz, em campo livre, no silêncio. Resultados: Os resultados apresentaram média de 69,5% para a lista de palavras monossílabas, 87,75% para a lista de palavras dissílabas, 89,92% para a lista de sílabas sem sentido e 92,5% para a lista de sentenças. Conclusão: O processo terapêutico aplicado, que incluiu o uso do AASI bilateral, foi extremamente satisfatório, uma vez que possibilitou o desenvolvimento máximo das habilidades auditivas.
ABSTRACT Purpose: To analyze speech perception in children with pre-lingual hearing loss with auditory neuropathy spectrum disorder users of bilateral hearing aid. Methods: This is a descriptive and exploratory study carried out at the Research Center Audiological (HRAC/USP). The study included four children aged between 8 years and 3 months and 12 years and 2 months. Lists of monosyllabic words, two syllables, nonsense words and sentences, the Infant Toddler-Meaningful Auditory Integration Scale (IT-MAIS) and the Meaningful Use of Speech Scale (MUSS), hearing, and language categories were used. All lists were applied in acoustic booth, with speakers, in free field, in silence. Results: The results showed an average 69.5% for the list of monosyllabic words, 87.75% for the list of two-syllable words, 89.92% for the list of nonsense syllables, and 92.5% for the list of sentences. Conclusion: The therapeutic process that includes the use of bilateral hearing aid was extremely satisfactory, since it allowed the maximum development of auditory skills.
Assuntos
Criança , Humanos , Masculino , Auxiliares de Audição , Perda Auditiva Central/reabilitação , Percepção da Fala , Percepção Auditiva , Implante Coclear , Perda Auditiva Central/cirurgia , Desenvolvimento da Linguagem , Inquéritos e QuestionáriosRESUMO
OBJECTIVE: In auditory neuropathy (AN) a dyssynchrony in the nerve conduction of the auditory nerve fibers is observed. Typically, patients with AN exhibit moderate to profound sensorineural hearing loss, and treatment using cochlear implants (CIs) or hearing aids should be performed as early as possible for a better hearing rehabilitation. The aim of this study is to evaluate the satisfaction level of patients with AN spectrum disorder treated using CIs. The Satisfaction with Amplification in Daily Life questionnaire was selected to evaluate 10 patients with AN treated using CIs. MATERIALS AND METHODS: Clinical study of patients with AN spectrum disorder submitted to CI. A retrospective data analysis, genetic and clinical evaluation in a tertiary referral center was done. RESULTS: The means of the subscales for positive effects, services and costs, negative factors, and personal image were 6.15, 4.6, 3.26, and 3.33, respectively. CONCLUSIONS: Patients with AN treated using CIs consider themselves satisfied.
Assuntos
Implantes Cocleares , Perda Auditiva Central/cirurgia , Satisfação do Paciente , Atividades Cotidianas , Criança , Pré-Escolar , Conexina 26 , Conexinas/genética , Feminino , Perda Auditiva Central/genética , Perda Auditiva Central/fisiopatologia , Humanos , Masculino , Mutação , Estudos Retrospectivos , Inquéritos e QuestionáriosRESUMO
Premature birth is a well-known risk factor for sensorineural hearing loss in general and auditory neuropathy in particular. However, relatively little is known about the underlying causes, in part because there are so few relevant histopathological studies. Here, we report on the analysis of hair cell loss patterns in 54 temporal bones from premature infants and a control group of 46 bones from full-term infants, all of whom spent time in the neonatal intensive care unit at the Hospital de Niños in San Jose, Costa Rica, between 1977 and 1993. The prevalence of significant hair cell loss was higher in the preterm group than the full-term group (41% vs. 28%, respectively). The most striking finding was the frequency of selective inner hair cell loss, an extremely rare histopathological pattern, in the preterm vs. the full-term babies (27% vs. 3%, respectively). The findings suggest that a common cause of non-genetic auditory neuropathy is selective loss of inner hair cells rather than primary damage to the cochlear nerve.