1.
J Pediatr Surg
; 35(8): 1269-71, 2000 Aug.
Artigo
em Inglês
| MEDLINE
| ID: mdl-10945711
RESUMO
The authors report a case of a virilizing adrenal tumor that developed in a 2-year-old child with Beckwith-Wiedemann syndrome (BWS). He had a fetal diagnosis of omphalocele and a history of neonatal adrenal cysts. The importance of prenatal diagnosis of BWS and postnatal follow-up of tumors is discussed. The differential diagnosis of adrenal pathologies occurring in BWS also is reviewed.